New insights into hereditary angio-oedema: Molecular diagnosis and therapy

Australasian Journal of Dermatology

Volumn 51, Issue 3, 2010, Pages 157-162

  Nagy, Nikoletta ^a   Grattan, Clive E ^b   McGrath, John A ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

^b GUY'S AND ST THOMAS' NHS FOUNDATION TRUST   (United Kingdom)

Author keywords

bradykinin; coagulation factor XII; genetic disease; oedema; skin

Indexed keywords

3 (6 ACETAMIDO 3 PYRIDYL) N [N [2,4 DICHLORO 3 [(2 METHYL 8 QUINOLINYL)OXYMETHYL]PHENYL] N METHYLAMINOCARBONYLMETHYL]ACRYLAMIDE; BLOOD CLOTTING FACTOR 12; BRADYKININ; BRADYKININ ANTAGONIST; BRADYKININ RECEPTOR; COMPLEMENT C1 INHIBITOR CONCENTRATE; COMPLEMENT COMPONENT C1Q; COMPLEMENT COMPONENT C1S INHIBITOR; COMPLEMENT COMPONENT C2; COMPLEMENT COMPONENT C4; COMPLEMENT INHIBITOR; DANAZOL; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; ECALLANTIDE; HISTAMINE; ICATIBANT; KALBITOR; KALLIKREIN; MEN 16132; OXANDROLONE; RECOMBINANT COMPLEMENT C1 INHIBITOR; RHUCIN; STANOZOLOL; TRANEXAMIC ACID; UNCLASSIFIED DRUG;

ANAPHYLAXIS; ANGIONEUROTIC EDEMA; C1NH GENE; CLINICAL FEATURE; DIAGNOSTIC PROCEDURE; DISEASE SEVERITY; F12 GENE; GENE; GENE MUTATION; GONADAL DISEASE; HUMAN; INJECTION SITE BURNING; INJECTION SITE PAIN; INJECTION SITE PRURITUS; INJECTION SITE SWELLING; LIVER CELL CARCINOMA; MENSTRUAL IRREGULARITY; MORBIDITY; MORTALITY; RARE DISEASE; REVIEW; SIDE EFFECT; URTICARIA; WEIGHT GAIN;

ANGIOEDEMAS, HEREDITARY; ANGIOTENSIN-CONVERTING ENZYME INHIBITORS; BRADYKININ; COMPLEMENT C1 INACTIVATOR PROTEINS; ESTROGENS; FACTOR XII; FEMALE; HUMANS; KALLIKREINS; MUTATION; RECEPTORS, BRADYKININ;

EID: 77955289381     PISSN: 00048380     EISSN: 14400960     Source Type: Journal    
DOI: 10.1111/j.1440-0960.2010.00649.x     Document Type: Review

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