Pathogenesis of ER storage disorders: Modulating russell body biogenesis by altering proximal and distal quality control

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Volumn 11, Issue 7, 2010, Pages 947-957

  Ronzoni, Riccardo ^a   Anelli, Tiziana ^a,b   Brunati, Martina ^a,b   Cortini, Margherita ^a,b   Fagioli, Claudio ^a   Sitia, Roberto ^a,b  

^a SAN RAFFAELE HOSPITAL   (Italy)

^b VITA SALUTE SAN RAFFAELE UNIVERSITY   (Italy)

Author keywords

Early secretory compartment; Endoplasmic reticulum; ERGIC; Protein condensation

Indexed keywords

CHAPERONE; CHAPERONE ERP44; CHAPERONE PDI; IMMUNOGLOBULIN LIGHT CHAIN; IMMUNOGLOBULIN M; IMMUNOGLOBULIN MU CHAIN; UNCLASSIFIED DRUG;

ARTICLE; BIOGENESIS; CELL STRUCTURE; CONTROLLED STUDY; EARLY SECRETORY COMPARTMENT; GENE OVEREXPRESSION; GOLGI COMPLEX; HUMAN; HUMAN CELL; IMMUNOGLOBULIN CONSTANT REGION; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN CONDENSATION; PROTEIN SECRETION; QUALITY CONTROL; ROUGH ENDOPLASMIC RETICULUM; RUSSELL BODY; SMOOTH ENDOPLASMIC RETICULUM;

ANIMALS; ENDOPLASMIC RETICULUM; HELA CELLS; HUMANS; IMMUNOGLOBULIN M; POLYMERS; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; PROTEINS; QUALITY CONTROL;

EID: 77954714045     PISSN: 13989219     EISSN: 16000854     Source Type: Journal    
DOI: 10.1111/j.1600-0854.2010.01071.x     Document Type: Article

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