Diaphragm displays early and progressive functional deficits in dysferlin-deficient mice

Muscle and Nerve

Volumn 42, Issue 1, 2010, Pages 22-29

  Barton, Elisabeth R ^a,b   Wang, Bing Jing ^a   Brisson, Becky K ^a,b   Sweeney, H Lee ^a,b  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Dysferlin; Fiber type; Mouse models; Muscle function; Muscular dystrophy

Indexed keywords

DYSFERLIN; MYOSIN HEAVY CHAIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIAPHRAGM; DISEASE PREDISPOSITION; ECCENTRIC MUSCLE CONTRACTION; FUNCTIONAL ASSESSMENT; LIMB GIRDLE MUSCULAR DYSTROPHY; LIMB GIRDLE MUSCULAR DYSTROPHY TYPE 2B; MEMBRANE RUPTURE; MIYOSHI MYOPATHY; MOUSE; MOUSE STRAIN; MUSCLE CELL; MUSCLE FORCE; MUSCLE INJURY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; SKELETAL MUSCLE;

ANIMALS; BLOTTING, WESTERN; DIAPHRAGM; ELECTROPHORESIS, POLYACRYLAMIDE GEL; FEMALE; ISOMETRIC CONTRACTION; MALE; MEMBRANE PROTEINS; MICE; MICE, INBRED A; MICE, INBRED C57BL; MICE, INBRED MDX; MICE, KNOCKOUT; MUSCLE CONTRACTION; MUSCLE FIBERS, SKELETAL; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES, LIMB-GIRDLE;

EID: 77954097959     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.21645     Document Type: Article

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