Muscle degeneration in neuraminidase 1-deficient mice results from infiltration of the muscle fibers by expanded connective tissue

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1802, Issue 7-8, 2010, Pages 659-672

  Zanoteli, Edmar ^a   de Vlekkert, Diantha van ^a   Bonten, Erik J ^a   Hu, Huimin ^a   Mann, Linda ^a   Gomero, Elida M ^a   Harris, A John ^b   Ghersi, Giulio ^c   d'Azzo, Alessandra ^a  

^a ST JUDE CHILDREN S RESEARCH HOSPITAL   (United States)

^b UNIVERSITY OF OTAGO   (New Zealand)

^c UNIVERSITY OF PALERMO   (Italy)

Author keywords

ECM; Lysosome; Metalloproteinase; Muscle biopsy; NEU1; Sialidosis

Indexed keywords

CATHEPSIN; CELL MARKER; COLLAGEN; GLYCOSIDASE; METALLOPROTEINASE; NEUROMINIDASE 1; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL INFILTRATION; CELL PROLIFERATION; CONNECTIVE TISSUE; CONTROLLED STUDY; CYTOSOL; DISEASE ASSOCIATION; ENZYME ACTIVITY; EPIMYSIUM; EXTRACELLULAR MATRIX; FIBROBLAST; LYSOSOME; MALE; MOUSE; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE DISEASE; MUSCLE INJURY; MYOPATHY; NONHUMAN; PERIMYSIUM; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEGRADATION; SARCOLEMMA; SIALIDOSIS; SKELETAL MUSCLE;

ANIMALS; APOPTOSIS; CELL MOVEMENT; CELL PROLIFERATION; CONNECTIVE TISSUE; EXTRACELLULAR MATRIX; FIBROBLASTS; MICE; MICE, KNOCKOUT; MUSCLE FIBERS, SKELETAL; MUSCULAR ATROPHY; MUSCULAR DYSTROPHY, ANIMAL; NECROSIS; NEURAMINIDASE; SARCOLEMMA;

ANIMALIA; MUS;

EID: 77953812943     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbadis.2010.04.002     Document Type: Article

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