Management of patients with factor V deficiency: Open issues from the challenging history of a woman with anaphylactic transfusion reactions

Haemophilia

Volumn 16, Issue 3, 2010, Pages 560-563

  Coppola, A ^a   Maruotti, G M ^a   Feola, G ^b   Catalano, A ^b   Quaglia, F ^a   Tomaiuolo, M ^c   Di Minno, M N D ^a   Cerbone, A M ^a   Margaglione, M ^c,d   Martinelli, P ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b S Luca Hospital   (Italy)

^c CASA SOLLIEVO DELLA SOFFERENZA HOSPITAL   (Italy)

^d UNIVERSITY OF FOGGIA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIHISTAMINIC AGENT; FRESH FROZEN PLASMA; HEMOSTATIC AGENT; ORAL CONTRACEPTIVE AGENT; RECOMBINANT BLOOD CLOTTING FACTOR 7A; STEROID; TRANEXAMIC ACID;

BLEEDING; BLOOD CLOTTING FACTOR 5 DEFICIENCY; BLOOD TRANSFUSION REACTION; CASE REPORT; DRUG HYPERSENSITIVITY; ERYTHROCYTE TRANSFUSION; FEMALE; FOLLICLE CYST; HEMOPERITONEUM; HUMAN; LAPAROTOMY; LETTER; MENORRHAGIA; PATIENT COMPLIANCE; PRIORITY JOURNAL;

ADULT; ANAPHYLAXIS; BLOOD TRANSFUSION; CESAREAN SECTION; CONTRACEPTIVES, ORAL; FACTOR V DEFICIENCY; FACTOR VIIA; FEMALE; FOLLICULAR CYST; HEMOPERITONEUM; HEMORRHAGE; HUMANS; MENSTRUATION; PLASMA; PREGNANCY; PREGNANCY OUTCOME; RECOMBINANT PROTEINS; YOUNG ADULT;

EID: 77953602528     PISSN: 13518216     EISSN: 13652516     Source Type: Journal    
DOI: 10.1111/j.1365-2516.2009.02147.x     Document Type: Letter

References (12)

1. Huang JN, Koerper MA. Factor V deficiency: a concise review. Haemophilia 2008, 14:1164-9.
2. Divanon F, Hecquard C, Borel-Derlon A. Experience with use of recombinant activated factor VII. J Clin Pharmacol Ther 2002, 27:133-8.
3. González-Boullosa R, Ocampo-Martínez R, Alárcon-Martin MJ, Suarez-Rodríguez M, Domínguez-Viguerra L, González Fajo G. The use of activated recombinant coagulation factor VII during haemarthroses and synovectomy in a patient with congenital severe factor V deficiency. Haemophilia 2005, 11:167-70.
4. Petros S, Fischer J, Mössner J, Schiefke I, Teich N. Treatment of massive cecal bleeding in a 28-year-old patient with homozygous factor V deficiency with activated factor VII. Z Gastroenterol 2008, 46:271-3.
5. Lee CA, Chi C, Pavord S. The obstetric and gyneaecological management of woman with inherited bleeding disorders - review with guidelines produced by a taskforce of UK Haemophilia Centre Doctors' Organization. Haemophilia 2006, 12:301-36.
6. Girolami A, Scandellari R, Lombardi AM, Girolami B, Bortoletto E, Zanon E. Pregnancy and oral contraceptives in factor V deficiency: a study of 22 patients (five homozygotes and 17 heterozygotes) and a review of the literature. Haemophilia 2005, 11:26-30.
7. Payne JH, Maclean RM, Hampton KK, Baxter AJ, Makris M. Haemoperitoneum associated with ovulation in women with inherited bleeding disorders: the case for conservative management and the role of the contraceptive pill. Haemophilia 2007, 13:93-7.
8. Pruss A, Kalus U, Radtke H. Universal leukodepletion of blood components results in a significant reduction of febrile non-hemolytic but not allergic transfusion reactions. Transfus Apheres Sci 2004, 30:41-6.
9. Santagostino E, Mancuso ME, Morfini M. Solvent/detergent plasma for prevention of bleeding in recessively inherited coagulation disorders: dosing, pharmacokinetics and clinical efficacy. Haematologica 2006, 91:634-9.
10. Franchini M, Lippi G, Montagnana M. Anaphylaxis in patients with congenital bleeding disorders and inhibitors. Blood Coagul Fibrinolysis 2009, 20:225-9.
11. Altisent C, Lozano M, Sol E. Dental extraction using rFVIIa in a patient with severe FV deficiency. Haemophilia 2000, 6:408.
12. Borel-Derlon A, Slaoui M, Le Querec A, Hugel B, Vos HL. Severe congenital factor V deficiency: successful treatment with recombinant factor VIIa in two brothers. Blood 2002, 100:107b. [abstract 3876]