Liver transplantation for inherited metabolic disorders of the liver

Current Opinion in Organ Transplantation

Volumn 15, Issue 3, 2010, Pages 269-276

  Moini, Maryam ^a   Mistry, Pramod ^b,c   Schilsky, Michael L ^b,c  

^a SHIRAZ UNIVERSITY OF MEDICAL SCIENCES   (Iran)

^b YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c YALE UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Familial amyloid polyneuropathy; Familial hypercholesterolemia; Glycogen storage disease; Hemochromatosis; Primary hyperoxaluria; Wilson disease

Indexed keywords

ACETYLCYSTEINE; APOLIPOPROTEIN B; FIBRINOGEN A ALPHA CHAIN; FIBRINOGEN VARIANT; HFE PROTEIN; LOW DENSITY LIPOPROTEIN; PREALBUMIN; UNCLASSIFIED DRUG;

ACUTE INTERMITTENT PORPHYRIA; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ANTISENSE THERAPY; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; DISEASE ASSOCIATION; FAMILIAL AMYLOIDOSIS; FAMILIAL HYPERCHOLESTEROLEMIA; GENE MUTATION; GLOMERULUS FILTRATION RATE; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 4; HEMOCHROMATOSIS; HUMAN; KIDNEY FAILURE; KIDNEY FUNCTION; KIDNEY TRANSPLANTATION; LIVER CELL CARCINOMA; LIVER FAILURE; LIVER FUNCTION TEST; LIVER METABOLISM; LIVER TRANSPLANTATION; METABOLIC DISORDER; OUTCOME ASSESSMENT; OXALOSIS 1; PHLEBOTOMY; QUALITY CONTROL; REVIEW; STEM CELL TRANSPLANTATION; SURVIVAL RATE; TREATMENT INDICATION; TYROSINEMIA; UREA CYCLE; WILSON DISEASE;

AMYLOIDOSIS, FAMILIAL; GLYCOGEN STORAGE DISEASE; HEMOCHROMATOSIS; HEPATOLENTICULAR DEGENERATION; HUMANS; HYPERLIPOPROTEINEMIA TYPE II; HYPEROXALURIA, PRIMARY; LIVER DISEASES; LIVER TRANSPLANTATION; METABOLISM, INBORN ERRORS; PATIENT SELECTION; PORPHYRIAS; TIME FACTORS; TREATMENT OUTCOME;

EID: 77953282998     PISSN: 10872418     EISSN: 15317013     Source Type: Journal    
DOI: 10.1097/MOT.0b013e3283399dbd     Document Type: Review

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