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Volumn 42, Issue 6, 2010, Pages 428-431

Ursodeoxycholic acid treatment in patients with cystic fibrosis at risk for liver disease

Author keywords

Cystic fibrosis; Liver disease; Meconium ileus; Ursodeoxycholic acid

Indexed keywords

URSODEOXYCHOLIC ACID; CHOLAGOGUE;

EID: 77952742282     PISSN: 15908658     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.dld.2009.07.022     Document Type: Article
Times cited : (27)

References (28)
  • 1
    • 0037460729 scopus 로고    scopus 로고
    • Cystic fibrosis
    • Ratjen F., Doring G. Cystic fibrosis. Lancet 2003, 361:681-689.
    • (2003) Lancet , vol.361 , pp. 681-689
    • Ratjen, F.1    Doring, G.2
  • 2
    • 0024423668 scopus 로고
    • Identification of the cystic fibrosis gene: genetic analysis
    • Karem B., Rommens J.M., Buchanan J.A., et al. Identification of the cystic fibrosis gene: genetic analysis. Science 1989, 245:1073-1080.
    • (1989) Science , vol.245 , pp. 1073-1080
    • Karem, B.1    Rommens, J.M.2    Buchanan, J.A.3
  • 3
    • 0025114509 scopus 로고
    • Expression and characterization of the cystic fibrosis transmembrane conductance regulator
    • Gregory R.J., Cheng S.H., Rich D.P., et al. Expression and characterization of the cystic fibrosis transmembrane conductance regulator. Nature 1990, 347:382-386.
    • (1990) Nature , vol.347 , pp. 382-386
    • Gregory, R.J.1    Cheng, S.H.2    Rich, D.P.3
  • 4
    • 13344282728 scopus 로고    scopus 로고
    • Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor
    • Rozmahel R., Wilschanski M., Matin A., et al. Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor. Nat Genet 1996, 12:280-287.
    • (1996) Nat Genet , vol.12 , pp. 280-287
    • Rozmahel, R.1    Wilschanski, M.2    Matin, A.3
  • 5
    • 0025782271 scopus 로고
    • Prevalence of liver disease in cystic fibrosis
    • Scott-Jupp R., Lama L., Tanner M.S. Prevalence of liver disease in cystic fibrosis. Arch Dis Child 1991, 6:698-701.
    • (1991) Arch Dis Child , vol.6 , pp. 698-701
    • Scott-Jupp, R.1    Lama, L.2    Tanner, M.S.3
  • 6
    • 9644283027 scopus 로고    scopus 로고
    • Liver involvement in cystic fibrosis: primary organ damage or innocent bystander?
    • Colombo C., Battezzati P.M. Liver involvement in cystic fibrosis: primary organ damage or innocent bystander?. J Hepatol 2004, 41:1041-1044.
    • (2004) J Hepatol , vol.41 , pp. 1041-1044
    • Colombo, C.1    Battezzati, P.M.2
  • 7
    • 0027134853 scopus 로고
    • Localization of the cystic fibrosis transmembrane conductance regulator in human bile duct epithelial cells
    • Cohn J.A., Strong T.V., Picciotto M.R., et al. Localization of the cystic fibrosis transmembrane conductance regulator in human bile duct epithelial cells. Gastroenterology 1993, 105:1857-1864.
    • (1993) Gastroenterology , vol.105 , pp. 1857-1864
    • Cohn, J.A.1    Strong, T.V.2    Picciotto, M.R.3
  • 8
    • 0035737827 scopus 로고    scopus 로고
    • Liver disease in children with cystic fibrosis
    • Diwakar V., Pearson L., Beath S. Liver disease in children with cystic fibrosis. Peadiatr Respir Rev 2001, 2:340-349.
    • (2001) Peadiatr Respir Rev , vol.2 , pp. 340-349
    • Diwakar, V.1    Pearson, L.2    Beath, S.3
  • 9
    • 0036895702 scopus 로고    scopus 로고
    • Liver disease in cystic fibrosis: a prospective study on incidence, risk factors, and outcome
    • Colombo C., Battezzati P.M., Crosignani A., et al. Liver disease in cystic fibrosis: a prospective study on incidence, risk factors, and outcome. Hepatology 2002, 36:1374-1382.
    • (2002) Hepatology , vol.36 , pp. 1374-1382
    • Colombo, C.1    Battezzati, P.M.2    Crosignani, A.3
  • 10
    • 0028212786 scopus 로고
    • Analysis of risk factors for the development of liver disease associated with cystic fibrosis
    • Colombo C., Apostolo M.G., Ferrari M., et al. Analysis of risk factors for the development of liver disease associated with cystic fibrosis. J Pediatr 1994, 24:393-399.
    • (1994) J Pediatr , vol.24 , pp. 393-399
    • Colombo, C.1    Apostolo, M.G.2    Ferrari, M.3
  • 11
    • 20444456274 scopus 로고    scopus 로고
    • Effects of liver transplantation on nutritional status of patients with cystic fibrosis
    • Colombo C., Costantini D., Rocchi A., et al. Effects of liver transplantation on nutritional status of patients with cystic fibrosis. Transplant International 2005, 18:246-255.
    • (2005) Transplant International , vol.18 , pp. 246-255
    • Colombo, C.1    Costantini, D.2    Rocchi, A.3
  • 12
    • 0027209627 scopus 로고
    • Hepatoprotective properties of ursodeoxycholic acid
    • Douglas M.H., Gurie M.V. Hepatoprotective properties of ursodeoxycholic acid. Gastroenterology 1993, 104:1865-1870.
    • (1993) Gastroenterology , vol.104 , pp. 1865-1870
    • Douglas, M.H.1    Gurie, M.V.2
  • 13
    • 0027179015 scopus 로고
    • Molecular aspects of membrane stabilization by ursodeoxycholate
    • Guldutuna S., Zimmer G., Imhof M., et al. Molecular aspects of membrane stabilization by ursodeoxycholate. Gastroenterology 1993, 104:1736-1744.
    • (1993) Gastroenterology , vol.104 , pp. 1736-1744
    • Guldutuna, S.1    Zimmer, G.2    Imhof, M.3
  • 14
    • 0025180712 scopus 로고
    • Effects of ursodeoxicholic acid treatment on nutrition and liver function in patients with cystic fibrosis and longstanding cholestasis
    • Cotting J., Lentze M., Reichen J. Effects of ursodeoxicholic acid treatment on nutrition and liver function in patients with cystic fibrosis and longstanding cholestasis. Gut 1990, 31:918-921.
    • (1990) Gut , vol.31 , pp. 918-921
    • Cotting, J.1    Lentze, M.2    Reichen, J.3
  • 15
    • 0030852495 scopus 로고    scopus 로고
    • Combined analysis of randomized controlled trials of ursodeoxicolic acid in primary biliary cirrhosis
    • Poupon R.E., Lindor K.D., Cauch-Dudek K., et al. Combined analysis of randomized controlled trials of ursodeoxicolic acid in primary biliary cirrhosis. Gastroenterology 1997, 113:884-890.
    • (1997) Gastroenterology , vol.113 , pp. 884-890
    • Poupon, R.E.1    Lindor, K.D.2    Cauch-Dudek, K.3
  • 16
    • 0024998297 scopus 로고
    • Effects of ursodeoxycolic acid therapy for liver disease associated with cystic fibrosis
    • Colombo C., Setchell K.D., Podda M., et al. Effects of ursodeoxycolic acid therapy for liver disease associated with cystic fibrosis. J Pediatr 1990, 117:482-489.
    • (1990) J Pediatr , vol.117 , pp. 482-489
    • Colombo, C.1    Setchell, K.D.2    Podda, M.3
  • 17
    • 0026718322 scopus 로고
    • Effects of ursodeoxycolic acid on liver function in patients with cystic fibrosis and chronic cholestasis
    • Galabert C., Monet J.C., Lengrand D., et al. Effects of ursodeoxycolic acid on liver function in patients with cystic fibrosis and chronic cholestasis. J Pediatr 1992, 121:138-141.
    • (1992) J Pediatr , vol.121 , pp. 138-141
    • Galabert, C.1    Monet, J.C.2    Lengrand, D.3
  • 18
    • 0026584970 scopus 로고
    • Scintigraphic documentation of an improvement in epatobiliary excretory function after treatment with ursodeoxicolic acid in patients with cystic fibrosis and associated liver disease
    • Colombo C., Castellani M.R., Balistreri W.F., et al. Scintigraphic documentation of an improvement in epatobiliary excretory function after treatment with ursodeoxicolic acid in patients with cystic fibrosis and associated liver disease. Hepatology 1992, 15:677-684.
    • (1992) Hepatology , vol.15 , pp. 677-684
    • Colombo, C.1    Castellani, M.R.2    Balistreri, W.F.3
  • 19
    • 0035079090 scopus 로고    scopus 로고
    • Long term prospective study of effect of ursodeoxicolic acid on cystic fibrosis-related liver disease
    • Nousia Arvanitakis S., Fotoulaki M., Economou H., et al. Long term prospective study of effect of ursodeoxicolic acid on cystic fibrosis-related liver disease. J Clin Gastroenterol 2001, 32:324-328.
    • (2001) J Clin Gastroenterol , vol.32 , pp. 324-328
    • Nousia Arvanitakis, S.1    Fotoulaki, M.2    Economou, H.3
  • 20
    • 19144371795 scopus 로고    scopus 로고
    • Ursodeoxycholic acid for liver disease associated with cystic fibrosis: a double-blind multicenter trial
    • Colombo C., Battezzati P.M., Podda M., et al. Ursodeoxycholic acid for liver disease associated with cystic fibrosis: a double-blind multicenter trial. Hepatology 1996.
    • (1996) Hepatology
    • Colombo, C.1    Battezzati, P.M.2    Podda, M.3
  • 21
    • 0036299705 scopus 로고    scopus 로고
    • Nutrition in patients with cystic fibrosis: a European Consensus
    • 1484-90
    • Sinaasappel M., Stern M., Littlewood J., et al. Nutrition in patients with cystic fibrosis: a European Consensus. J Cystic Fibrosis 2002, 1:51-75. 1484-90.
    • (2002) J Cystic Fibrosis , vol.1 , pp. 51-75
    • Sinaasappel, M.1    Stern, M.2    Littlewood, J.3
  • 22
    • 33748091347 scopus 로고    scopus 로고
    • Clinical outcome of cystic fibrosis presenting with or without meconium ileus: a matched cohort study
    • Munck A., Gerardin M., Alberti C., et al. Clinical outcome of cystic fibrosis presenting with or without meconium ileus: a matched cohort study. J Pediatr Surg 2006, 41:1556-1560.
    • (2006) J Pediatr Surg , vol.41 , pp. 1556-1560
    • Munck, A.1    Gerardin, M.2    Alberti, C.3
  • 23
    • 0035172675 scopus 로고    scopus 로고
    • The impact of meconium ileus on the clinical course of children with cystic fibrosis
    • Evans A.K.C., Fitzgerald, McKay K.O. The impact of meconium ileus on the clinical course of children with cystic fibrosis. Eur Respir J 2001, 18:784-789.
    • (2001) Eur Respir J , vol.18 , pp. 784-789
    • Evans, A.K.C.1    Fitzgerald2    McKay, K.O.3
  • 24
    • 4544231975 scopus 로고    scopus 로고
    • Longitudinal pulmonary status of cystic fibrosis children with meconium ileus
    • Li Z., Lai H.J., Kosorok M.R., et al. Longitudinal pulmonary status of cystic fibrosis children with meconium ileus. Pediatr Pulmonol 2004, 38:277-284.
    • (2004) Pediatr Pulmonol , vol.38 , pp. 277-284
    • Li, Z.1    Lai, H.J.2    Kosorok, M.R.3
  • 25
    • 0033984416 scopus 로고    scopus 로고
    • Nutritional status of patients with cystic fibrosis with meconium ileus: a comparison with patients without meconium ileus and diagnosed early through neonatal screening
    • Lai H.C., Kosorok M.R., Laxova A., et al. Nutritional status of patients with cystic fibrosis with meconium ileus: a comparison with patients without meconium ileus and diagnosed early through neonatal screening. Pediatrics 2000, 105:53-61.
    • (2000) Pediatrics , vol.105 , pp. 53-61
    • Lai, H.C.1    Kosorok, M.R.2    Laxova, A.3
  • 26
    • 0142075838 scopus 로고    scopus 로고
    • Meconium Ileus in CF patients is not a risk factor for clinical deterioration and survival: the Israeli multi-center study
    • Efrati O., Nir J., Fraser D., et al. Meconium Ileus in CF patients is not a risk factor for clinical deterioration and survival: the Israeli multi-center study. Eur J Gastroenterol Hepatol 2003, 15:1073-1078.
    • (2003) Eur J Gastroenterol Hepatol , vol.15 , pp. 1073-1078
    • Efrati, O.1    Nir, J.2    Fraser, D.3
  • 27
    • 34247543025 scopus 로고    scopus 로고
    • Liver disease as risk factor for cystic fibrosis-related diabetes development
    • Minicucci L., Lorini R., Giannattasio A., et al. Liver disease as risk factor for cystic fibrosis-related diabetes development. Acta Paediatr 2007, 96:736-739.
    • (2007) Acta Paediatr , vol.96 , pp. 736-739
    • Minicucci, L.1    Lorini, R.2    Giannattasio, A.3
  • 28
    • 35648934624 scopus 로고    scopus 로고
    • Ursodeoxycholic acid stimulates cholangiocyte fluid secretion in mice via CFTR-dependent ATP secretion
    • Fiorotto R., Spirlì C., Fabris L., et al. Ursodeoxycholic acid stimulates cholangiocyte fluid secretion in mice via CFTR-dependent ATP secretion. Gastroenterology 2007, 133:1603-1613.
    • (2007) Gastroenterology , vol.133 , pp. 1603-1613
    • Fiorotto, R.1    Spirlì, C.2    Fabris, L.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.