Outpatient treatment of propionic acidemia-associated hyperammonemia with N-carbamoyl-L-glutamate in an infant

Clinical Therapeutics

Volumn 32, Issue 4, 2010, Pages 710-713

  Soyucen, Erdogan ^a   Demirci, Esra ^a   Aydin, Ahmet ^a  

^a ISTANBUL UNIVERSITY   (Turkey)

Author keywords

Hyperammonemia; N carbamoyl l glutamate; Organic acidemia; Propionic acidemia; Treatment

Indexed keywords

CARGLUMIC ACID; CARNITINE; GLUTAMIC ACID DERIVATIVE; N CARBAMOYL GLUTAMIC ACID; PROPIONIC ACID; UNCLASSIFIED DRUG;

ARTICLE; CASE REPORT; FEMALE; FOLLOW UP; HOSPITALIZATION; HUMAN; HYPERAMMONEMIA; INFANT; INVASIVE PROCEDURE; OUTPATIENT CARE; PROPIONIC ACIDEMIA; PROTEIN RESTRICTION;

CARNITINE; DIET; FEMALE; GLUTAMATES; HUMANS; HYPERAMMONEMIA; INFANT; PROPIONIC ACIDEMIA;

EID: 77952513239     PISSN: 01492918     EISSN: 1879114X     Source Type: Journal    
DOI: 10.1016/j.clinthera.2010.04.004     Document Type: Article

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