Perioperative management of Glanzmann's syndrome: How we did it!

Blood Coagulation and Fibrinolysis

Volumn 21, Issue 3, 2010, Pages 283-284

  Depner, Christian ^a   Schmid, Roger ^a   Kirchhoff, Philipp ^a   Oertli, Daniel ^a  

^a UNIVERSITY HOSPITAL BASEL   (Switzerland)

Author keywords

Morbus Glanzmann; Perioperative management of thrombasthenia Glanzmann; Thrombasthenia Glanzmann

Indexed keywords

FIBRINOGEN; FIBRINOGEN RECEPTOR; RECOMBINANT BLOOD CLOTTING FACTOR 7A; TRANEXAMIC ACID;

ADULT; ANAMNESIS; ARTICLE; BLEEDING TENDENCY; BOLUS INJECTION; CASE REPORT; DISEASE ASSOCIATION; GLANZMANN DISEASE; HEMATOMA; HUMAN; INGUINAL HERNIA; INGUINAL REGION; LOADING DRUG DOSE; MALE; PAIN; PARTIAL THROMBOPLASTIN TIME; PATIENT CARE; PERIOPERATIVE PERIOD; PRIORITY JOURNAL; SURGICAL RISK; SURGICAL TECHNIQUE; THROMBIN TIME; THROMBOCYTE ADHESION; THROMBOCYTE AGGREGATION; THROMBOCYTE DYSFUNCTION; THROMBOCYTE TRANSFUSION; TREATMENT DURATION; TREATMENT INDICATION; TREATMENT OUTCOME;

ANTIFIBRINOLYTIC AGENTS; FACTOR VIIA; HERNIA, INGUINAL; HUMANS; MALE; PLATELET TRANSFUSION; RECOMBINANT PROTEINS; THROMBASTHENIA; TRANEXAMIC ACID; YOUNG ADULT;

EID: 77950266822     PISSN: 09575235     EISSN: None     Source Type: Journal    
DOI: 10.1097/MBC.0b013e328330e683     Document Type: Article

References (16)

1. George JN, Caen JP, Nurden AT. Glanzmann's thrombasthenia: the spectrum of clinical disease. Blood 1990; 75:1383-1395.
2. Glanzman E. Hereditäre hämorrhagische thrombasthenia. Ein beitrag zur pathologie der bluttplattchen. 88[Jarbuch der Kinderheilkunde]. Jarbuch der Kinderheilkunde 1918; 88:1-42. Ref Type: Generic.
3. Vuckovic SA. Glanzmann's thrombasthenia revisited. J Emerg Med 1996; 14:299-303.
4. Bolton-Maggs PH, Chalmers EA, Collins PW, Harrison P, Kitchen S, Liesner RJ, et al. A review of inherited platelet disorders with guidelines for their management on behalf of the UKHCDO. Br J Haematol 2006; 135:603-633.
5. Ruiz C, Liu CY, Sun QH, Sigaud-Fiks M, Fressinaud E, Muller JY, et al. A point mutation in the cysteine-rich domain of glycoprotein (GP) IIIa results in the expression of a GPIIb-IIIa ({alpha}IIb{beta}3) integrin receptor locked in a high-affinity state and a Glanzmann thrombasthenia-like phenotype. Blood 2001; 98:2432-2441.
6. French DL, Coller BS. Hematologically important mutations: Glanzmann thrombasthenia. Blood Cells Mol Dis 1997; 23:39-51.
7. Nair S, Ghosh K, Kulkarni B, Shetty S, Mohanty D. Glanzmann's thrombasthenia: updated. Platelets 2002; 13:387-393.
8. d'Oiron R, Menart C, Trzeciak MC, Nurden P, Fressinaud E, Dreyfus M, et al. Use of recombinant factor VIIa in 3 patients with inherited type I Glanzmann's thrombasthenia undergoing invasive procedures. Thromb Haemost 2000; 83:644-647.
9. Saxena R, Kannan M. Glanzmann's thrombasthenia: an overview. Clin Appl Thromb Hemost 2009; 15:152-165.
10. Bisch FC, Bowen KJ, Hanson BS, Kudryk VL, Billman MA. Dental considerations for a Glanzmann's thrombasthenia patient: case report. J Periodontol 1996; 67:536-540.
11. Lombardo VT, Sottilotta G. Recombinant activated factor VII combined with desmopressin in preventing bleeding from dental extraction in a patient with Glanzmann's thrombasthenia. Clin Appl Thromb Hemost 2006; 12:115-116.
12. Uzunlar HI, Eroglu A, Senel AC, Bostan H, Erciyes N. A patient with Glanzmann's thrombasthenia for emergent abdominal surgery. Anesth Analg 2004; 99:1258-1260.
13. Bougie DW, Wilker PR, Wuitschick ED, Curtis BR, Malik M, Levine S, et al. Acute thrombocytopenia after treatment with tirofiban or eptifibatide is associated with antibodies specific for ligand-occupied GPIIb/IIIa. Blood 2002; 100:2071-2076.
14. Poon MC. Use of recombinant factor VIIa in hereditary bleeding disorders. Curr Opin Hematol 2001; 8:312-318.
15. Poon MC, Zotz R, Di Minno G, Abrams ZS, Knudsen JB, Laurian Y. Glanzmann's thrombasthenia treatment: a prospective observational registry on the use of recombinant human activated factor VII and other hemostatic agents. Semin Hematol 2006; 43:S33-S36.
16. Bellucci S, Devergie A, Gluckman E, Tobelem G, Lethielleux P, Benbunan M, et al. Complete correction of Glanzmann's thrombasthenia by allogeneic bone-marrow transplantation. Br J Haematol 1985; 59:635-641.