Identification of proteins in the ceroid-like autofluorescent aggregates from liver lysosomes of Beige, a mouse model for human Chediak-Higashi syndrome

Molecular Genetics and Metabolism

Volumn 99, Issue 4, 2010, Pages 389-395

  Zhang, Huiwen ^a   Mahuran, Don J ^a,b   Callahan, John W ^a,c  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

^c UNIVERSITY OF TORONTO   (Canada)

Author keywords

Autofluorescence; Autophagy; Ceroid; Chediak Higashi syndrome

Indexed keywords

CEROID; GLUCOSE REGULATED PROTEIN 78; PROTEIN; SOLUBLE MICROTUBULAR ASSOCIATED PROTEIN 1; UNCLASSIFIED DRUG;

ACIDITY; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; AUTOFLUORESCENCE; AUTOPHAGY; CHEDIAK HIGASHI SYNDROME; CONTROLLED STUDY; CYTOSOL; ENDOPLASMIC RETICULUM; FIBROBLAST; HUMAN; HUMAN CELL; ION TRAP MASS SPECTROMETRY; LIGHT CHAIN; LIVER LYSOSOME; MITOCHONDRION; MOUSE; NONHUMAN; PEROXISOME; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN LOCALIZATION;

ANIMALS; AUTOPHAGY; CELLS, CULTURED; CEROID; CHEDIAK-HIGASHI SYNDROME; DISEASE MODELS, ANIMAL; FLUORESCENCE; LIVER; LYSOSOMES; MASS SPECTROMETRY; MICE; PROTEINS; PROTEOMICS;

EID: 77649337555     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2009.12.009     Document Type: Article

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