Occurrence of an anomalous endocytic compartment in fibroblasts from Sandhoff disease patients

Molecular and Cellular Biochemistry

Volumn 335, Issue 1-2, 2010, Pages 273-282

  Tancini, Brunella ^a   Magini, Alessandro ^a   Latterini, Loredana ^a   Urbanelli, Lorena ^a   Ciccarone, Virginia ^a   Elisei, Fausto ^a   Emiliani, Carla ^a  

^a UNIVERSITY OF PERUGIA   (Italy)

Author keywords

Endocytic compartment; GM2 storage; Lysosomal storage disease; Sandhoff disease

Indexed keywords

ARTICLE; CELL METABOLISM; CELL ORGANELLE; CELL VACUOLE; CONTROLLED STUDY; ENDOCYTOSIS; ENDOSOME; FIBROBLAST; HUMAN; HUMAN CELL; LYSOSOME; PATHOGENESIS; SANDHOFF DISEASE; SIGNAL TRANSDUCTION;

BETA-N-ACETYLHEXOSAMINIDASES; CELLS, CULTURED; ENDOCYTOSIS; ENDOSOMES; FIBROBLASTS; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; HYDROGEN-ION CONCENTRATION; LYSOSOMES; SANDHOFF DISEASE;

EID: 75949093765     PISSN: 03008177     EISSN: 15734919     Source Type: Journal    
DOI: 10.1007/s11010-009-0277-0     Document Type: Article

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