메뉴 건너뛰기




Volumn 77, Issue 4, 2010, Pages 267-269

Excessive activation of the complement system in atypical hemolytic uremic syndrome: Is it ready for prime time

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENT FACTOR I; ECULIZUMAB;

EID: 75749119748     PISSN: 00852538     EISSN: 15231755     Source Type: Journal    
DOI: 10.1038/ki.2009.467     Document Type: Note
Times cited : (5)

References (13)
  • 1
    • 63049087674 scopus 로고    scopus 로고
    • Mechanisms of microvascular thrombosis in thrombotic thrombocytopenic purpura
    • Tsai HM. Mechanisms of microvascular thrombosis in thrombotic thrombocytopenic purpura. Kidney Int Suppl 2009; 75 (Suppl 112): S11-S14.
    • (2009) Kidney Int Suppl , vol.75 , Issue.SUPPL. 112
    • Tsai, H.M.1
  • 2
    • 62449341861 scopus 로고    scopus 로고
    • Autoantibodies in haemolytic uraemic syndrome (HUS)
    • Skerka C, Jozsi M, Zipfel PF et al. Autoantibodies in haemolytic uraemic syndrome (HUS). Thromb Haemost 2009; 101: 227-232.
    • (2009) Thromb Haemost , vol.101 , pp. 227-232
    • Skerka, C.1    Jozsi, M.2    Zipfel, P.F.3
  • 3
    • 67651166873 scopus 로고    scopus 로고
    • Thrombomodulin mutations in atypical hemolytic-uremic syndrome
    • Delvaeye M, Noris M, DeV A et al.Thrombomodulin mutations in atypical hemolytic-uremic syndrome. N Engl J Med 2009; 361: 345-357.
    • (2009) N Engl J Med , vol.361 , pp. 345-357
    • Delvaeye, M.1    Noris, M.2    Dev, A.3
  • 4
    • 19444369542 scopus 로고    scopus 로고
    • Complement factor I: A susceptibility gene for atypical haemolytic uraemic syndrome
    • online doi:10.1136/jmg.2004.019083
    • Fremeaux-Bacchi V, Dragon-Durey MA, Blouin J et al. Complement factor I: a susceptibility gene for atypical haemolytic uraemic syndrome. J Med Genet [online 2004; 41: e84; doi:10.1136/jmg.2004.019083.
    • (2004) J Med Genet , vol.41
    • Fremeaux-Bacchi, V.1    Dragon-Durey, M.A.2    Blouin, J.3
  • 6
    • 75749153964 scopus 로고    scopus 로고
    • Mutations in components of complement influence the outcome of Factor I-associated atypical hemolytic uremic syndrome
    • Bienaime F, Dragon-Durey M-A, Regnier CH et al. Mutations in components of complement influence the outcome of Factor I-associated atypical hemolytic uremic syndrome. Kidney Int 2010; 77: 339-349.
    • (2010) Kidney Int , vol.77 , pp. 339-349
    • Bienaime, F.1    Dragon-Durey, M.-A.2    Regnier, C.H.3
  • 7
    • 67650508077 scopus 로고    scopus 로고
    • T h e high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome
    • Dragon-Durey MA, Blanc C, Marliot F et al. T h e high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome. J Med Genet 2009; 46: 447-450.
    • (2009) J Med Genet , vol.46 , pp. 447-450
    • Dragon-Durey, M.A.1    Blanc, C.2    Marliot, F.3
  • 8
    • 70349441306 scopus 로고    scopus 로고
    • F a c t o r H-related protein 1 (CFHR-1) inhibits complement C5 convertase activity and terminal complex formation
    • Heinen S, Hartmann A,Lauer N et al. F a c t o r H-related protein 1 (CFHR-1) inhibits complement C5 convertase activity and terminal complex formation. Blood 2009; 114: 2439-2447.
    • (2009) Blood , vol.114 , pp. 2439-2447
    • Heinen, S.1    Hartmann Alauer, N.2
  • 9
    • 70349437186 scopus 로고    scopus 로고
    • Complement regulators and inhibitory proteins
    • Zipfel PF, Skerka C. Complement regulators and inhibitory proteins. Nat Rev Immunol 2009; 9: 729-740.
    • (2009) Nat Rev Immunol , vol.9 , pp. 729-740
    • Zipfel, P.F.1    Skerka, C.2
  • 10
    • 38849102544 scopus 로고    scopus 로고
    • Factor i is required for the development of membranoproliferative glomerulonephritis in factor H-deficient mice
    • Rose KL, Paixao-Cavalcante D, Fish J et al. Factor I is required for the development of membranoproliferative glomerulonephritis in factor H-deficient mice. J Clin Invest 2008; 118: 608-618.
    • (2008) J Clin Invest , vol.118 , pp. 608-618
    • Rose, K.L.1    Paixao-Cavalcante, D.2    Fish, J.3
  • 11
    • 41149171882 scopus 로고    scopus 로고
    • Deletion of CFHR3 and CFHR1 genes in age-related macular degeneration
    • Spencer KL, Hauser MA, Olson LM et al. Deletion of CFHR3 and CFHR1 genes in age-related macular degeneration. Hum Mol Genet 2008; 17: 971-977.
    • (2008) Hum Mol Genet , vol.17 , pp. 971-977
    • Spencer, K.L.1    Hauser, M.A.2    Olson, L.M.3
  • 12
    • 59449107473 scopus 로고    scopus 로고
    • Eculizumab for atypical hemolytic-uremic syndrome
    • Nurnberger J, Philipp T, Witzke O et al. Eculizumab for atypical hemolytic-uremic syndrome. N Engl J Med 2009; 360: 542-544.
    • (2009) N Engl J Med , vol.360 , pp. 542-544
    • Nurnberger, J.1    Philipp, T.2    Witzke, O.3
  • 13
    • 59449088846 scopus 로고    scopus 로고
    • Eculizumab for congenital atypical hemolytic-uremic syndrome
    • Gruppo RA, Rother RP. Eculizumab for congenital atypical hemolytic-uremic syndrome. N Engl J Med 2009; 360: 544-546.
    • (2009) N Engl J Med , vol.360 , pp. 544-546
    • Gruppo, R.A.1    Rother, R.P.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.