Prevalence of sickle cell disease in a northeastern region of the Democratic Republic of Congo: What impact on transfusion policy?

Transfusion Medicine

Volumn 20, Issue 1, 2010, Pages 62-65

  Agasa, B ^a   Bosunga, K ^a   Opara, A ^a   Tshilumba, K ^a   Dupont, E ^b   Vertongen, F ^c   Cotton, F ^c   Gulbis, B ^c  

^a UNIVERSITY OF KISANGANI   (Congo)

^b ERASME HOSPITAL   (Belgium)

^c UNIVERSITÉ LIBRE DE BRUXELLES   (Belgium)

Author keywords

Kisangani; Neonatal; Screening; Sickle cell disease

Indexed keywords

ARTICLE; ATTENTION; AUTHORITY; BLOOD TRANSFUSION; CONTROLLED STUDY; DEMOCRATIC REPUBLIC CONGO; FEMALE; HEALTH CENTER; HUMAN; INFECTION RISK; ISOELECTRIC FOCUSING; MAJOR CLINICAL STUDY; MALE; NEWBORN; NEWBORN SCREENING; PREVALENCE; PUBLIC HEALTH; SICKLE CELL ANEMIA; SICKLE CELL TRAIT; UMBILICAL CORD BLOOD;

ANEMIA, SICKLE CELL; BETA-GLOBINS; BLOOD TRANSFUSION; BLOOD-BORNE PATHOGENS; DEMOCRATIC REPUBLIC OF THE CONGO; FEMALE; FETAL BLOOD; GENOTYPE; HEALTH POLICY; HEALTH SERVICES NEEDS AND DEMAND; HUMANS; INFANT, NEWBORN; INFECTION CONTROL; MALE; NEONATAL SCREENING; PREVALENCE;

EID: 74049134297     PISSN: 09587578     EISSN: 13653148     Source Type: Journal    
DOI: 10.1111/j.1365-3148.2009.00943.x     Document Type: Article

References (16)

1. Afenyi-Annan, A., Willis, M.S., Konrad, T.R. & Lottenberg, R. (2007) Blood bank management of sickle cell patients at comprehensive sickle cell centers. Transfusion, 47, 2089 2097.
2. Akinyanju, O.O., Otaigbe, A.I. & Ibidapo, M.O. (2005) Outcome of holistic care in Nigerian patients with sickle cell anaemia. Clinical and Laboratory Haematology, 27, 195 199.
3. Angastiniotis, M. & Modell, B. (1998). Global epidemiology of haemoglobin disorders. Annals of New York Academic Sciences, 850, 251 269.
4. Batina, A., Kabemba, S. & Malengela, R. (2007) Infectious markers among blood donors in Democratic Republic of Congo (DRC). Revue Medicale de Bruxelles, 28, 145 149.
5. Field, S.P. & Allain, J.P. (2007) Transfusion in sub-Saharan Africa: does a Western model fit? Journal of Clinical Pathology, 60, 1073 1075.
6. Gulbis, B., Tshilolo, L., Cotton, F., Lin, C. & Vertongen, F. (1999) Newborn screening for haemoglobinopathies: the Brussels experience. Journal of Medical Screening, 6, 11 15.
7. Makani, J., Williams, T.N. & Marsh, K. (2007) Sickle cell disease: burden and research priorities. Annal of Tropical Medicine and Parasitology, 101, 3 14.
8. Marcucci, C., Madjdpour, C. & Spahn, D.R. (2004) Allogeneic blood transfusions: benefit, risks and clinical indications in countries with a low or high human development index. British Medical Bulletin, 70, 15 28.
9. Monteny, V.A. (1963) The ABO blood groups of the Congolese North-eastern peoples. Annales de la Societe Belge de Medecine Tropicale, 43, 777 793.
10. Munyanganizi, R., Cotton, F., Vertongen, F. & Gulbis, B. (2006) Red blood cell disorders in Rwandese neonates: screening for sickle cell disease and glucose-6-phosphate dehydrogenase deficiency. Journal of Medical Screening, 13, 129 131.
11. Rahimy, M.C., Gangbo, A., Ahouignan, G., Adjou, R., Deguenon, C., Goussanou, S. & Alihonou, E. (2003) Effect of a comprehensive clinical care program on disease course in severely ill children with sickle cell anemia in a sub-Saharan African setting. Blood, 102, 834 838.
12. Republique Democratique du Congo. Annuaire Sanitaire, 2006.
13. Serjeant, G. & Ndugwa, C. 2003) Sickle cell disease in Uganda: a time for action. East African Medical Journal, 80, 384 387.
14. Tshilolo, L. 2003) La drepanocytose en Republique Democratique du Congo: aperccu sur la situation actuelle et perspectives d'avenir. Congo Medical, 3, 1044 1051.
15. Tshilolo, L., Kafando, E., Sawadgo, M., Cotton, F., Vertongen, F., Ferster, A. & Gulbis, B. 2008) Neonatal screening and clinical care programmes for sickle cell disorders in sub-Saharan Africa: Lessons from pilot studies. Public Health, 122, 933 941.
16. Weatherall, D. & Clegg, J. 2001) Inherited haemoglobin disorders: an increasing global health problem. Bulletin of the World Health Organization, 79, 704 712.