Malignant variant of sclerosing perivascular epithelioid cell tumor arising in the Adnexa

International Journal of Gynecological Pathology

Volumn 28, Issue 6, 2009, Pages 589-593

  Ramaiah, Srinivas ^a   Ganesan, Raji ^a   Mangham, D Charles ^b   McNally, Orla ^c   Klys, Howard S ^c   Hirschowitz, Lynn ^a  

^a BIRMINGHAM WOMEN S HOSPITAL   (United Kingdom)

^b ROYAL ORTHOPAEDIC HOSPITAL   (United Kingdom)

^c MUSGROVE PARK HOSPITAL   (United Kingdom)

Author keywords

Adnexa; Malignant; PEComa; Sclerosing

Indexed keywords

ALKALINE PHOSPHATASE; DESMIN; LACTATE DEHYDROGENASE; MYOGLOBIN; SMOOTH MUSCLE ACTIN;

ABDOMINAL HYSTERECTOMY; ADULT; ALKALINE PHOSPHATASE BLOOD LEVEL; ANEMIA; ARTICLE; BLISTER; BRONCHIECTASIS; CANCER DIAGNOSIS; CANCER MORTALITY; CANCER SURGERY; CASE REPORT; CHOLECYSTECTOMY; COMPUTER ASSISTED TOMOGRAPHY; DYSPNEA; EOSINOPHIL; EPITHELIOID CELL; EPITHELIUM TUMOR; FEMALE; FEMALE GENITAL SYSTEM; HERNIA INCARCERATION; HIATUS HERNIA; HUMAN; IMMUNOHISTOCHEMISTRY; LACTATE DEHYDROGENASE BLOOD LEVEL; LIVER METASTASIS; LUNG LOBE; LUNG METASTASIS; LYMPH NODE BIOPSY; MALIGNANT SCLEROSING PERIVASCULAR EPITHELIOID CELL TUMOR; MALIGNANT TRANSFORMATION; METASTASIS; MICROSCOPY; MITOSIS; NECROSIS; NUCLEAR MAGNETIC RESONANCE IMAGING; OVARY; PELVIS LYMPH NODE; PERITONEAL BIOPSY; PRIORITY JOURNAL; SALPINGOOOPHORECTOMY; THORAX PAIN; THORAX RADIOGRAPHY; TREATMENT REFUSAL; TUMOR CELL; UTERINE TUBE; UTERUS MYOMA; FATALITY; LIVER TUMOR; LUNG TUMOR; METABOLISM; MIDDLE AGED; PARKINSON DISEASE; PATHOLOGY; PERIVASCULAR EPITHELIOID CELL TUMOR; RHEUMATOID ARTHRITIS; UTERUS CANCER;

ADNEXA UTERI; ARTHRITIS, RHEUMATOID; CHOLECYSTECTOMY; FATAL OUTCOME; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; LIVER NEOPLASMS; LUNG NEOPLASMS; MIDDLE AGED; PARKINSON DISEASE; PERIVASCULAR EPITHELIOID CELL NEOPLASMS; UTERINE NEOPLASMS;

EID: 73949128023     PISSN: 02771691     EISSN: None     Source Type: Journal    
DOI: 10.1097/PGP.0b013e3181a3a4de     Document Type: Article

References (13)

1. Folpe AL. Neoplasms with perivascular epithelioid cell differentiation (PEComas). In: Fletcher C, Unni K, Mertens F, eds. International Academy of Pathology: Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon, France: IARC Press; 2002:221-222
2. Bonetti F, Pea M, Martignoni G, et al. PEC and sugar. Am J Surg Pathol 1992;16:307-308
3. Martignoni G, Pea M, Reghellin D, et al. PEComas: the past, the present and the future. Virchows Arch 2008;452:119-132
4. Hornick JL, Fletcher CD. Sclerosing PEComa: clinicopathologic analysis of a distinctive variant with a predilection for the retroperitoneum. Am J Surg Pathol 2008;32:493-501.
5. Vang R, Kempson RL. Perivascular epithelioid cell tumor ("PEComa") of the uterus: a subset of HMB-45-positive epithelioid mesenchymal neoplasms with an uncertain relationship to pure smooth muscle tumors. Am J Surg Pathol 2002;26:1-13.
6. Folpe AL, Mentzel T, Lehr HA, et al. Perivascular epithelioid cell neoplasms of soft tissue and gynecologic origin: a clinicopathologic study of 26 cases and review of the literature. Am J Surg Pathol 2005;29:1558-1575
7. Anderson AE, Yang X, Young RH. Epithelioid angiomyolipoma of the ovary: a case report and literature review. Int J Gynecol Pathol 2002;21:69-73.
8. Tazelaar HD, Batts KP, Srigley JR. Primary extrapulmonary sugar tumor (PEST): a report of four cases. Mod Pathol 2001; 14:615-622
9. Ong LY, Hwang WS, Wong A, et al. Perivascular epithelioid cell tumour of the vagina in an 8 year old girl. J Pediatr Surg 2007;42:564-566
10. Lian DW, Chuah KL, Cheng MH, et al. Malignant perivascular epithelioid cell tumour of the fibula: a report and a short review of bone perivascular epithelioid cell tumour. J Clin Pathol 2008;61:1127-1129
11. Silva EG, Deavers MT, Bodurka DC, et al. Uterine epithelioid leiomyosarcomas with clear cells: reactivity with HMB-45 and the concept of PEComa. Am J Surg Pathol 2004;28: 244-249
12. Fink D, Marsden DE, Edwards L, et al. Malignant perivascular epithelioid cell tumor (PEComa) arising in the broad ligament. Int J Gynecol Cancer 2004;14:1036-1039
13. Liang SX, Pearl M, Liu J, et al. "Malignant" uterine perivascular epithelioid cell tumor, pelvic lymph node lymphangioleiomyomatosis, and gynecological pecomatosis in a patient with tuberous sclerosis: a case report and review of the literature. Int J Gynecol Pathol 2008;27:86-90.