-
1
-
-
0038158316
-
The role of the C terminus and Na+/H+ exchanger regulatory factor in the functional expression of cystic fibrosis transmembrane conductance regulator in nonpolarized cells and epithelia
-
Benharouga M, Sharma M, So J, Haardt M, Drzymala L, Popov M, Schwapach B, et al. (2003) The role of the C terminus and Na+/H+ exchanger regulatory factor in the functional expression of cystic fibrosis transmembrane conductance regulator in nonpolarized cells and epithelia. J Biol Chem 278:22079-22089
-
(2003)
J Biol Chem
, vol.278
, pp. 22079-22089
-
-
Benharouga, M.1
Sharma, M.2
So, J.3
Haardt, M.4
Drzymala, L.5
Popov, M.6
Schwapach, B.7
-
2
-
-
0032911839
-
Intracellular CFTR: Localization and function
-
Bradbury NA (1999) Intracellular CFTR: localization and function. Physiol Rev 79(suppl 1):175-191
-
(1999)
Physiol Rev
, vol.79
, Issue.SUPPL. 1
, pp. 175-191
-
-
Bradbury, N.A.1
-
3
-
-
0028322331
-
Biochemical and biophysical identification of cystic fibrosis transmembrane conductance regulator chloride channels as components of endocytic clathrin-coated vesicles
-
Bradbury NA, Cohn JA, Venglarik CJ, Bridges RJ (1994) Biochemical and biophysical identification of cystic fibrosis transmembrane conductance regulator chloride channels as components of endocytic clathrin-coated vesicles. J Biol Chem 269:8296-8302
-
(1994)
J Biol Chem
, vol.269
, pp. 8296-8302
-
-
Bradbury, N.A.1
Cohn, J.A.2
Venglarik, C.J.3
Bridges, R.J.4
-
4
-
-
0026581842
-
Regulation of plasma membrane recycling by CFTR
-
Bradbury NA, Jilling T, Berta G, Sorscher EJ, Bridges RJ, Kirk KL (1992) Regulation of plasma membrane recycling by CFTR. Science 256:530-532
-
(1992)
Science
, vol.256
, pp. 530-532
-
-
Bradbury, N.A.1
Jilling, T.2
Berta, G.3
Sorscher, E.J.4
Bridges, R.J.5
Kirk, K.L.6
-
5
-
-
34147180489
-
Facial nerve palsy associated with a low serum vitamin A level in an infant with cystic fibrosis
-
Cameron C, Lodes MW, Gershan WM (2007) Facial nerve palsy associated with a low serum vitamin A level in an infant with cystic fibrosis. J Cyst Fibros 6:241-243
-
(2007)
J Cyst Fibros
, vol.6
, pp. 241-243
-
-
Cameron, C.1
Lodes, M.W.2
Gershan, W.M.3
-
8
-
-
0023277545
-
Single-step method of RNA isolation by acid guanidinium thiocyanate-phenol-chloroform extraction
-
Chomczynski P, Sacchi N (1987) Single-step method of RNA isolation by acid guanidinium thiocyanate-phenol-chloroform extraction. Anal Biochem 162:156-159
-
(1987)
Anal Biochem
, vol.162
, pp. 156-159
-
-
Chomczynski, P.1
Sacchi, N.2
-
9
-
-
34248663955
-
The single-step method of RNA isolation by acid guanidinium thiocyanate-phenol-chloroform extraction: Twenty-something years on
-
Chomczynski P, Sacchi N (2006) The single-step method of RNA isolation by acid guanidinium thiocyanate-phenol-chloroform extraction: twenty-something years on. Nat Protoc 1:581-585
-
(2006)
Nat Protoc
, vol.1
, pp. 581-585
-
-
Chomczynski, P.1
Sacchi, N.2
-
10
-
-
0028014372
-
Vacuolar ATPase activity is required for endosomal carrier vesicle formation
-
Clague MJ, Urbe S, Aniento F, Gruenberg J (1994) Vacuolar ATPase activity is required for endosomal carrier vesicle formation. J Biol Chem 269:21-24
-
(1994)
J Biol Chem
, vol.269
, pp. 21-24
-
-
Clague, M.J.1
Urbe, S.2
Aniento, F.3
Gruenberg, J.4
-
11
-
-
0025858593
-
Amyloid precursor protein and ubiquitin immunoreactivity in dystrophic axons is not unique to Alzheimer's disease
-
Cochran E, Bacci B, Chen Y, Patton A, Gambetti P, Autilio-Gambetti L (1991) Amyloid precursor protein and ubiquitin immunoreactivity in dystrophic axons is not unique to Alzheimer's disease. Am J Pathol 139:485-489
-
(1991)
Am J Pathol
, vol.139
, pp. 485-489
-
-
Cochran, E.1
Bacci, B.2
Chen, Y.3
Patton, A.4
Gambetti, P.5
Autilio-Gambetti, L.6
-
12
-
-
0027928745
-
CFTR expression and chloride secretion in polarized immortal human bronchial epithelial cells
-
Cozens AL, Yezzi MJ, Kunzelmann K, Ohrui T, Chin L, Eng K, Finkbeiner WE, et al. (1994) CFTR expression and chloride secretion in polarized immortal human bronchial epithelial cells. Am J Respir Cell Mol Biol 10:38-47
-
(1994)
Am J Respir Cell Mol Biol
, vol.10
, pp. 38-47
-
-
Cozens, A.L.1
Yezzi, M.J.2
Kunzelmann, K.3
Ohrui, T.4
Chin, L.5
Eng, K.6
Finkbeiner, W.E.7
-
13
-
-
0026547330
-
Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia
-
Denning GM, Ostedgaard LS, Cheng SH, Smith AE, Welsh MJ (1992) Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia. J Clin Invest 89:339-349
-
(1992)
J Clin Invest
, vol.89
, pp. 339-349
-
-
Denning, G.M.1
Ostedgaard, L.S.2
Cheng, S.H.3
Smith, A.E.4
Welsh, M.J.5
-
14
-
-
33748146503
-
CFTR regulates phagosome acidification in macrophages and alters bactericidal activity
-
Di A, Brown ME, Deriy LV, Li C, Szeto FL, Chen Y, Huang P, et al. (2006) CFTR regulates phagosome acidification in macrophages and alters bactericidal activity. Nat Cell Biol 8:933-944
-
(2006)
Nat Cell Biol
, vol.8
, pp. 933-944
-
-
Di, A.1
Brown, M.E.2
Deriy, L.V.3
Li, C.4
Szeto, F.L.5
Chen, Y.6
Huang, P.7
-
15
-
-
0026687233
-
Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR
-
Egan M, Flotte T, Afione S, Solow R, Zeitlin PL, Carter BJ, Guggino WB (1992) Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR. Nature 358:581-584
-
(1992)
Nature
, vol.358
, pp. 581-584
-
-
Egan, M.1
Flotte, T.2
Afione, S.3
Solow, R.4
Zeitlin, P.L.5
Carter, B.J.6
Guggino, W.B.7
-
17
-
-
0026951303
-
Submucosal glands are the predominant site of CFTR expression in the human bronchus
-
Engelhardt JF, Yankaskas JR, Ernst SA, Yang Y, Marino CR, Boucher RC, Cohn JA, et al. (1992) Submucosal glands are the predominant site of CFTR expression in the human bronchus. Nat Genet 2:240-248
-
(1992)
Nat Genet
, vol.2
, pp. 240-248
-
-
Engelhardt, J.F.1
Yankaskas, J.R.2
Ernst, S.A.3
Yang, Y.4
Marino, C.R.5
Boucher, R.C.6
Cohn, J.A.7
-
18
-
-
0026528274
-
CFTR illegitimate transcription in lymphoid cells: Quantification and applications to the investigation of pathological transcripts
-
Fonknechten N, Chelly J, Lepercq J, Kahn A, Kaplan JC, Kitzis A, Chomel JC (1992) CFTR illegitimate transcription in lymphoid cells: quantification and applications to the investigation of pathological transcripts. Hum Genet 88:508-512
-
(1992)
Hum Genet
, vol.88
, pp. 508-512
-
-
Fonknechten, N.1
Chelly, J.2
Lepercq, J.3
Kahn, A.4
Kaplan, J.C.5
Kitzis, A.6
Chomel, J.C.7
-
19
-
-
33847357783
-
Misassembled mutant DeltaF508 CFTR in the distal secretory pathway alters cellular lipid trafficking
-
Gentzsch M, Choudhury A, Chang XB, Pagano RE, Riordan JR (2007) Misassembled mutant DeltaF508 CFTR in the distal secretory pathway alters cellular lipid trafficking. J Cell Sci 120:447-455
-
(2007)
J Cell Sci
, vol.120
, pp. 447-455
-
-
Gentzsch, M.1
Choudhury, A.2
Chang, X.B.3
Pagano, R.E.4
Riordan, J.R.5
-
20
-
-
0033857616
-
Cystic fibrosis patients with and without central nervous system complications following lung transplantation
-
Goldstein AB, Goldstein LS, Perl MK, Haug MT, Arroliga AC, Stillwell PC (2000) Cystic fibrosis patients with and without central nervous system complications following lung transplantation. Pediatr Pulmonol 30:203-206
-
(2000)
Pediatr Pulmonol
, vol.30
, pp. 203-206
-
-
Goldstein, A.B.1
Goldstein, L.S.2
Perl, M.K.3
Haug, M.T.4
Arroliga, A.C.5
Stillwell, P.C.6
-
21
-
-
0027051076
-
A multifunctional aqueous channel formed by CFTR
-
Hasegawa H, Skach W, Baker O, Calayag MC, Lingappa V, Verkman AS (1992) A multifunctional aqueous channel formed by CFTR. Science 258:1477-1479
-
(1992)
Science
, vol.258
, pp. 1477-1479
-
-
Hasegawa, H.1
Skach, W.2
Baker, O.3
Calayag, M.C.4
Lingappa, V.5
Verkman, A.S.6
-
22
-
-
4344586376
-
The nucleolus is involved in mRNA export from the nucleus in fission yeast
-
Ideue T, Azad AK, Yoshida J, Matsusaka T, Yanagida M, Ohshima Y, Tani T (2004) The nucleolus is involved in mRNA export from the nucleus in fission yeast. J Cell Sci 117:2887-2895
-
(2004)
J Cell Sci
, vol.117
, pp. 2887-2895
-
-
Ideue, T.1
Azad, A.K.2
Yoshida, J.3
Matsusaka, T.4
Yanagida, M.5
Ohshima, Y.6
Tani, T.7
-
23
-
-
0345329603
-
Glutathione and signal transduction in the mammalian CNS
-
Janaky R, Ogita K, Pasqualotto BA, Bains JS, Oja SS, Yoneda Y, Shaw CA (1999) Glutathione and signal transduction in the mammalian CNS. J Neurochem 73:889-902
-
(1999)
J Neurochem
, vol.73
, pp. 889-902
-
-
Janaky, R.1
Ogita, K.2
Pasqualotto, B.A.3
Bains, J.S.4
Oja, S.S.5
Yoneda, Y.6
Shaw, C.A.7
-
24
-
-
0031889465
-
Cellular heterogeneity of CFTR expression and function in the lung: Implications for gene therapy of cystic fibrosis
-
Jiang Q, Engelhardt JF (1998) Cellular heterogeneity of CFTR expression and function in the lung: implications for gene therapy of cystic fibrosis. Eur J Hum Genet 6:12-31
-
(1998)
Eur J Hum Genet
, vol.6
, pp. 12-31
-
-
Jiang, Q.1
Engelhardt, J.F.2
-
25
-
-
0030891243
-
Cystic fibrosis mRNA expression in rat brain: Cerebral cortex and medial preoptic area
-
Johannesson M, Bogdanovic N, Nordqvist AC, Hjelte L, Schalling M (1997) Cystic fibrosis mRNA expression in rat brain: cerebral cortex and medial preoptic area. Neuroreport 8:535-539
-
(1997)
Neuroreport
, vol.8
, pp. 535-539
-
-
Johannesson, M.1
Bogdanovic, N.2
Nordqvist, A.C.3
Hjelte, L.4
Schalling, M.5
-
26
-
-
33847061634
-
Two populations of Thy1-positive mesenchymal cells regulate in vitro maturation of hepatic progenitor cells
-
Kamo N, Yasuchika K, Fujii H, Hoppo T, Machimoto T, Ishii T, Fujita N, et al. (2007) Two populations of Thy1-positive mesenchymal cells regulate in vitro maturation of hepatic progenitor cells. Am J Physiol Gastrointest Liver Physiol 292:G526-534
-
(2007)
Am J Physiol Gastrointest Liver Physiol
, vol.292
-
-
Kamo, N.1
Yasuchika, K.2
Fujii, H.3
Hoppo, T.4
Machimoto, T.5
Ishii, T.6
Fujita, N.7
-
27
-
-
33947401472
-
Autophagosome-lysosome fusion depends on the pH in acidic compartments in CHO cells
-
Kawai A, Uchiyama H, Takano S, Nakamura N, Ohkuma S (2007) Autophagosome-lysosome fusion depends on the pH in acidic compartments in CHO cells. Autophagy 3:154-157
-
(2007)
Autophagy
, vol.3
, pp. 154-157
-
-
Kawai, A.1
Uchiyama, H.2
Takano, S.3
Nakamura, N.4
Ohkuma, S.5
-
28
-
-
0014824298
-
Increased intracranial pressure associated with probable vitamin A deficiency in cystic fibrosis
-
Keating JP, Feigin RD (1970) Increased intracranial pressure associated with probable vitamin A deficiency in cystic fibrosis. Pediatrics 46:41-46
-
(1970)
Pediatrics
, vol.46
, pp. 41-46
-
-
Keating, J.P.1
Feigin, R.D.2
-
29
-
-
0024423668
-
Identification of the cystic fibrosis gene: Genetic analysis
-
Kerem B, Rommens JM, Buchanan JA, Markiewicz D, Cox TK, Chakravarti A, Buchwald M, et al. (1989) Identification of the cystic fibrosis gene: genetic analysis. Science 245:1073-1080
-
(1989)
Science
, vol.245
, pp. 1073-1080
-
-
Kerem, B.1
Rommens, J.M.2
Buchanan, J.A.3
Markiewicz, D.4
Cox, T.K.5
Chakravarti, A.6
Buchwald, M.7
-
30
-
-
0038369932
-
CFTR directly mediates nucleotide-regulated glutathione flux
-
Kogan I, Ramjeesingh M, Li C, Kidd JF,Wang Y, Leslie EM, Cole SP, et al. (2003) CFTR directly mediates nucleotide-regulated glutathione flux. EMBO J 22:1981-1989
-
(2003)
EMBO J
, vol.22
, pp. 1981-1989
-
-
Kogan, I.1
Ramjeesingh, M.2
Li, C.3
Kidd, J.F.4
Wang, Y.5
Leslie, E.M.6
Cole, S.P.7
-
31
-
-
0345873303
-
Reduced expression of the cystic fibrosis transmembrane conductance regulator gene in the hypothalamus of patients with Alzheimer's disease
-
Lahousse SA, Stopa EG, Mulberg AE, de la Monte SM (2003) Reduced expression of the cystic fibrosis transmembrane conductance regulator gene in the hypothalamus of patients with Alzheimer's disease. J Alzheimers Dis 5:455-462
-
(2003)
J Alzheimers Dis
, vol.5
, pp. 455-462
-
-
Lahousse, S.A.1
Stopa, E.G.2
Mulberg, A.E.3
de la Monte, S.M.4
-
32
-
-
0028889864
-
A novel, simple, reliable, and sensitive method for multiple immunoenzyme staining: Use of microwave oven heating to block antibody crossreactivity and retrieve antigens
-
Lan HY, Mu W, Nikolic-Paterson DJ, Atkins RC (1995) A novel, simple, reliable, and sensitive method for multiple immunoenzyme staining: use of microwave oven heating to block antibody crossreactivity and retrieve antigens. J Histochem Cytochem 43:97-102
-
(1995)
J Histochem Cytochem
, vol.43
, pp. 97-102
-
-
Lan, H.Y.1
Mu, W.2
Nikolic-Paterson, D.J.3
Atkins, R.C.4
-
33
-
-
0026777811
-
The cystic fibrosis transmembrane regulator is present and functional in endosomes. Role as a determinant of endosomal pH
-
LukacsGL, ChangXB, KartnerN,RotsteinOD, Riordan JR,Grinstein S (1992) The cystic fibrosis transmembrane regulator is present and functional in endosomes. Role as a determinant of endosomal pH. J Biol Chem 267:14568-14572
-
(1992)
J Biol Chem
, vol.267
, pp. 14568-14572
-
-
Lukacs, G.L.1
Chang, X.B.2
Kartner, N.3
Rotstein, O.D.4
Riordan, J.R.5
Grinstein, S.6
-
34
-
-
15744386914
-
CFTR: More than just a chloride channel
-
Mehta A (2005) CFTR: more than just a chloride channel. Pediatr Pulmonol 39:292-298
-
(2005)
Pediatr Pulmonol
, vol.39
, pp. 292-298
-
-
Mehta, A.1
-
35
-
-
0031045778
-
Functional expression and apical localization of the cystic fibrosis transmembrane conductance regulator in MDCK I cells
-
Mohamed A, Ferguson D, Seibert FS, Cai HM, Kartner N, Grinstein S, Riordan JR, et al. (1997) Functional expression and apical localization of the cystic fibrosis transmembrane conductance regulator in MDCK I cells. Biochem J 322:259-265
-
(1997)
Biochem J
, vol.322
, pp. 259-265
-
-
Mohamed, A.1
Ferguson, D.2
Seibert, F.S.3
Cai, H.M.4
Kartner, N.5
Grinstein, S.6
Riordan, J.R.7
-
36
-
-
0029615502
-
Downregulation by progesterone of CFTR expression in endometrial epithelial cells: A study by competitive RT-PCR
-
Mularoni A, Beck L, Sadir R, Adessi GL, Nicollier M (1995) Downregulation by progesterone of CFTR expression in endometrial epithelial cells: a study by competitive RT-PCR. Biochem Biophys Res Commun 217:1105-1111
-
(1995)
Biochem Biophys Res Commun
, vol.217
, pp. 1105-1111
-
-
Mularoni, A.1
Beck, L.2
Sadir, R.3
Adessi, G.L.4
Nicollier, M.5
-
37
-
-
0029090214
-
Expression and localization of the cystic fibrosis transmembrane conductance regulator mRNA and its protein in rat brain
-
Mulberg AE, Resta LP, Wiedner EB, Altschuler SM, Jefferson DM, Broussard DL (1995) Expression and localization of the cystic fibrosis transmembrane conductance regulator mRNA and its protein in rat brain. J Clin Invest 96:646-652
-
(1995)
J Clin Invest
, vol.96
, pp. 646-652
-
-
Mulberg, A.E.1
Resta, L.P.2
Wiedner, E.B.3
Altschuler, S.M.4
Jefferson, D.M.5
Broussard, D.L.6
-
38
-
-
0032484636
-
Cystic fibrosis transmembrane conductance regulator expression in human hypothalamus
-
Mulberg AE, Weyler RT, Altschuler SM, Hyde TM (1998) Cystic fibrosis transmembrane conductance regulator expression in human hypothalamus. Neuroreport 9:141-144
-
(1998)
Neuroreport
, vol.9
, pp. 141-144
-
-
Mulberg, A.E.1
Weyler, R.T.2
Altschuler, S.M.3
Hyde, T.M.4
-
39
-
-
0027934029
-
Cystic fibrosis transmembrane conductance regulator protein expression in brain
-
Mulberg AE, Wiedner EB, Bao X, Marshall J, Jefferson DM, Altschuler SM (1994) Cystic fibrosis transmembrane conductance regulator protein expression in brain. Neuroreport 5:1684-1688
-
(1994)
Neuroreport
, vol.5
, pp. 1684-1688
-
-
Mulberg, A.E.1
Wiedner, E.B.2
Bao, X.3
Marshall, J.4
Jefferson, D.M.5
Altschuler, S.M.6
-
40
-
-
0032810262
-
Characterization of CFTR expression in a human pulmonary mucoepidermoid carcinoma cell line, NCI-H292 cells
-
Nagayama S, Kai H, Okiyoneda T, Horikawa S, Miyata T (1999) Characterization of CFTR expression in a human pulmonary mucoepidermoid carcinoma cell line, NCI-H292 cells. FEBS Lett 455:215-218
-
(1999)
FEBS Lett
, vol.455
, pp. 215-218
-
-
Nagayama, S.1
Kai, H.2
Okiyoneda, T.3
Horikawa, S.4
Miyata, T.5
-
41
-
-
0029063514
-
Purification and characterization of recombinant cystic fibrosis transmembrane conductance regulator from Chinese hamster ovary and insect cells
-
O'Riordan CR, Erickson A, Bear C, Li C, Manavalan P, Wang KX, Marshall J, et al. (1995) Purification and characterization of recombinant cystic fibrosis transmembrane conductance regulator from Chinese hamster ovary and insect cells. J Biol Chem 270:17033-17043
-
(1995)
J Biol Chem
, vol.270
, pp. 17033-17043
-
-
O'Riordan, C.R.1
Erickson, A.2
Bear, C.3
Li, C.4
Manavalan, P.5
Wang, K.X.6
Marshall, J.7
-
42
-
-
33748654201
-
CFTR expression in human neutrophils and the phagolysosomal chlorination defect in cystic fibrosis
-
Painter RG, Valentine VG, Lanson NA Jr, Leidal K, Zhang Q, Lombard G, Thompson C, et al. (2006) CFTR expression in human neutrophils and the phagolysosomal chlorination defect in cystic fibrosis. Biochemistry 45:10260-10269
-
(2006)
Biochemistry
, vol.45
, pp. 10260-10269
-
-
Painter, R.G.1
Valentine, V.G.2
Lanson Jr, N.A.3
Leidal, K.4
Zhang, Q.5
Lombard, G.6
Thompson, C.7
-
43
-
-
0032226945
-
Expression of the cystic fibrosis transmembrane conductance regulator (CFTR) mRNA in normal and pathological adult human epididymis
-
SalamehWA
-
Patrizio P, SalamehWA (1998) Expression of the cystic fibrosis transmembrane conductance regulator (CFTR) mRNA in normal and pathological adult human epididymis. J Reprod Fertil Suppl 53:261-270
-
(1998)
J Reprod Fertil
, Issue.SUPPL. 53
, pp. 261-270
-
-
Patrizio, P.1
-
44
-
-
0030610528
-
Bafilomycin A1 treatment retards transferrin receptor recycling more than bulk membrane recycling
-
Presley JF, Mayor S, McGraw TE, Dunn KW, Maxfield FR (1997) Bafilomycin A1 treatment retards transferrin receptor recycling more than bulk membrane recycling. J Biol Chem 272:13929-13936
-
(1997)
J Biol Chem
, vol.272
, pp. 13929-13936
-
-
Presley, J.F.1
Mayor, S.2
McGraw, T.E.3
Dunn, K.W.4
Maxfield, F.R.5
-
45
-
-
0028236014
-
Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel
-
Prince LS, Workman RB Jr, Marchase RB (1994) Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel. Proc Natl Acad Sci USA 91:5192-5196
-
(1994)
Proc Natl Acad Sci USA
, vol.91
, pp. 5192-5196
-
-
Prince, L.S.1
Workman Jr, R.B.2
Marchase, R.B.3
-
46
-
-
0028305440
-
Vacuolar ATPase inactivation blocks recycling to the trans-Golgi network from the plasma membrane
-
Reaves B, Banting G (1994) Vacuolar ATPase inactivation blocks recycling to the trans-Golgi network from the plasma membrane. FEBS Lett 345:61-66
-
(1994)
FEBS Lett
, vol.345
, pp. 61-66
-
-
Reaves, B.1
Banting, G.2
-
47
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan JR, Rommens JM, Kerem B, Alon N, Rozmahel R, Grzelczak Z, Zielenski J, et al. (1989) Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 245:1066-1073
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
Alon, N.4
Rozmahel, R.5
Grzelczak, Z.6
Zielenski, J.7
-
48
-
-
0024403962
-
Initial treatment of cystic fibrosis. Frequency of transient bulging fontanel
-
Roach ES, Sinal SH (1989) Initial treatment of cystic fibrosis. Frequency of transient bulging fontanel. Clin Pediatr (Phila) 28:371-373
-
(1989)
Clin Pediatr (Phila)
, vol.28
, pp. 371-373
-
-
Roach, E.S.1
Sinal, S.H.2
-
49
-
-
0032912589
-
Structure and function of the CFTR chloride channel
-
Sheppard DN, Welsh MJ (1999) Structure and function of the CFTR chloride channel. Physiol Rev 79(suppl 1):23-45
-
(1999)
Physiol Rev
, vol.79
, Issue.SUPPL. 1
, pp. 23-45
-
-
Sheppard, D.N.1
Welsh, M.J.2
-
50
-
-
0026645366
-
cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia
-
Smith JJ, Welsh MJ (1992) cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia. J Clin Invest 89:1148-1153
-
(1992)
J Clin Invest
, vol.89
, pp. 1148-1153
-
-
Smith, J.J.1
Welsh, M.J.2
-
51
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
Stutts MJ, Canessa CM, Olsen JC, Hamrick M, Cohn JA, Rossier BC, Boucher RC (1995) CFTR as a cAMP-dependent regulator of sodium channels. Science 269:847-850
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
Rossier, B.C.6
Boucher, R.C.7
-
52
-
-
0028356865
-
Differential cellular expression of cystic fibrosis transmembrane regulator in human reproductive tissues. Clues for the infertility in patients with cystic fibrosis
-
Tizzano EF, Silver MM, Chitayat D, Benichou JC, Buchwald M (1994) Differential cellular expression of cystic fibrosis transmembrane regulator in human reproductive tissues. Clues for the infertility in patients with cystic fibrosis. Am J Pathol 144:906-914
-
(1994)
Am J Pathol
, vol.144
, pp. 906-914
-
-
Tizzano, E.F.1
Silver, M.M.2
Chitayat, D.3
Benichou, J.C.4
Buchwald, M.5
-
54
-
-
0025787393
-
In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator
-
BuchwaldM
-
Trezise AE, BuchwaldM(1991) In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator. Nature 353:434-437
-
(1991)
Nature
, vol.353
, pp. 434-437
-
-
Trezise, A.E.1
-
55
-
-
0025978377
-
Caroli's disease associated with hepatolithiasis: A case report and review of the Japanese literature
-
Tsunoda T, Furui J, Yamada M, Eto T, Ura K, Matsumoto T, Segawa T, et al. (1991) Caroli's disease associated with hepatolithiasis: a case report and review of the Japanese literature. Gastroenterol Jpn 26:74-79
-
(1991)
Gastroenterol Jpn
, vol.26
, pp. 74-79
-
-
Tsunoda, T.1
Furui, J.2
Yamada, M.3
Eto, T.4
Ura, K.5
Matsumoto, T.6
Segawa, T.7
-
56
-
-
33748488451
-
Evidence that CFTR is expressed in rat tracheal smooth muscle cells and contributes to bronchodilation
-
Vandebrouck C, Melin P, Norez C, Robert R, Guibert C, Mettey Y, Becq F (2006) Evidence that CFTR is expressed in rat tracheal smooth muscle cells and contributes to bronchodilation. Respir Res 7:113
-
(2006)
Respir Res
, vol.7
, pp. 113
-
-
Vandebrouck, C.1
Melin, P.2
Norez, C.3
Robert, R.4
Guibert, C.5
Mettey, Y.6
Becq, F.7
-
57
-
-
0029160297
-
Transport from late endosomes to lysosomes, but not sorting of integral membrane proteins in endosomes, depends on the vacuolar proton pump
-
van Weert AW, Dunn KW, Gueze HJ, Maxfield FR, Stoorvogel W (1995) Transport from late endosomes to lysosomes, but not sorting of integral membrane proteins in endosomes, depends on the vacuolar proton pump. J Cell Biol 130:821-834
-
(1995)
J Cell Biol
, vol.130
, pp. 821-834
-
-
van Weert, A.W.1
Dunn, K.W.2
Gueze, H.J.3
Maxfield, F.R.4
Stoorvogel, W.5
-
58
-
-
0032861250
-
CFTR is functionally active in GnRH-expressing GT1-7 hypothalamic neurons
-
Weyler RT, Yurko-Mauro KA, Rubenstein R, Kollen WJ, Reenstra W, Altschuler SM, Egan M, et al. (1999) CFTR is functionally active in GnRH-expressing GT1-7 hypothalamic neurons. Am J Physiol 277:C563-571
-
(1999)
Am J Physiol
, vol.277
-
-
Weyler, R.T.1
Yurko-Mauro, K.A.2
Rubenstein, R.3
Kollen, W.J.4
Reenstra, W.5
Altschuler, S.M.6
Egan, M.7
|