Successful renal transplantation in factor H autoantibody associated HUS with CFHR1 and 3 deficiency and CFH variant G2850T: Case report

American Journal of Transplantation

Volumn 10, Issue 1, 2010, Pages 168-172

  Waters, A M ^a   Pappworth, I ^b   Marchbank, K ^b   Bockenhauer, D ^a   Tullus, K ^a   Pickering, M C ^c   Strain, L ^b   Sebire, N ^a   Shroff, R ^a   Marks, S D ^a   Goodship, T H J ^b   Rees, L ^a  

^a GREAT ORMOND STREET HOSPITAL   (United Kingdom)

^b NEWCASTLE UNIVERSITY   (United Kingdom)

^c IMPERIAL COLLEGE LONDON   (United Kingdom)

Author keywords

Factor H; Hemolytic uremic syndrome

Indexed keywords

AUTOANTIBODY; BASILIXIMAB; COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C4; COMPLEMENT FACTOR H; COMPLEMENT FACTOR H RECEPTOR 1; COMPLEMENT FACTOR H RECEPTOR 3; COMPLEMENT RECEPTOR; CORTICOSTEROID; CREATININE; FRESH FROZEN PLASMA; HEMOGLOBIN; INTERLEUKIN 2 RECEPTOR; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PREDNISOLONE; RITUXIMAB; UNCLASSIFIED DRUG;

ADJUVANT THERAPY; ANTIBODY DETECTION; ARTICLE; CASE REPORT; CENTRAL VENOUS CATHETER; CHILD; COMPLEMENT ACTIVATION; COMPLEMENT DISORDER; COMPLEMENT FACTOR H RECEPTOR 1 DEFICIENCY; COMPLEMENT FACTOR H RECEPTOR 3 DEFICIENCY; CREATININE BLOOD LEVEL; DRUG MEGADOSE; ENZYME LINKED IMMUNOSORBENT ASSAY; ESCHERICHIA COLI O157; EXON; FECES ANALYSIS; FEMALE; FIBROSING ALVEOLITIS; GENE AMPLIFICATION; GENE DELETION; GENE SEQUENCE; GENETIC VARIABILITY; GLOMERULUS; HEMODIALYSIS; HEMOGLOBIN BLOOD LEVEL; HEMOLYTIC UREMIC SYNDROME; HUMAN; IMMUNOSUPPRESSIVE TREATMENT; KIDNEY ALLOGRAFT; KIDNEY BIOPSY; KIDNEY DYSFUNCTION; KIDNEY TRANSPLANTATION; LETHARGY; PALLOR; PLASMAPHERESIS; PRIORITY JOURNAL; RECURRENT DISEASE; SCHOOL CHILD; THROMBOCYTE COUNT; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; TREATMENT DURATION; TREATMENT RESPONSE;

AMINO ACID SUBSTITUTION; AUTOANTIBODIES; BLOOD PROTEINS; CHILD; COMPLEMENT C3B INACTIVATOR PROTEINS; COMPLEMENT FACTOR H; FEMALE; GENETIC VARIATION; HEMOLYTIC-UREMIC SYNDROME; HUMANS; IMMUNOSUPPRESSIVE AGENTS; KIDNEY TRANSPLANTATION; POLYMORPHISM, SINGLE NUCLEOTIDE;

EID: 72549110489     PISSN: 16006135     EISSN: 16006143     Source Type: Journal    
DOI: 10.1111/j.1600-6143.2009.02870.x     Document Type: Article

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