The heterozygous Lemd3 +/GT mouse is not a murine model for osteopoikilosis in humans

Calcified Tissue International

Volumn 85, Issue 6, 2009, Pages 546-551

  Dheedene, Annelies ^a   Deleye, Steven ^b   Hellemans, Jan ^a   Staelens, Steven ^b   Vandenberghe, Stefaan ^b   Mortier, Geert ^a  

^a GHENT UNIVERSITY HOSPITAL   (Belgium)

^b GHENT UNIVERSITY   (Belgium)

Author keywords

Buschke Ollendorff syndrome; LEMD3; MicroCT; Osteopoikilosis; Transgenic mouse

Indexed keywords

RECEPTOR REGULATED SMAD PROTEIN; TRANSFORMING GROWTH FACTOR BETA1;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE DYSPLASIA; BUSCHKE OLLENDORFF SYNDROME; CONTROLLED STUDY; CORTICAL BONE; DISEASE MODEL; EMBRYONIC STEM CELL; FEMALE; FEMUR; GENE; HETEROZYGOTE; HIGH RESOLUTION COMPUTER TOMOGRAPHY; HYPEROSTOSIS; LEMD3 GENE; LONG BONE; LOSS OF FUNCTION MUTATION; MICRO-COMPUTED TOMOGRAPHY; MOUSE; NEWBORN; NONHUMAN; OSTEOSCLEROSIS; PRIORITY JOURNAL; TRABECULAR BONE;

ANIMALS; BONE AND BONES; DISEASE MODELS, ANIMAL; HETEROZYGOTE; HUMANS; MEMBRANE PROTEINS; MICE; MUTATION; NUCLEAR PROTEINS; OSTEOPOIKILOSIS;

EID: 72449138054     PISSN: 0171967X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00223-009-9305-z     Document Type: Article

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