Reduction of lysine intake while avoiding malnutrition - Major goals and major problems in dietary treatment of glutaryl-CoA dehydrogenase deficiency

Journal of Inherited Metabolic Disease

Volumn 27, Issue 6, 2004, Pages 903-910

  Müller, Edith ^a   Kolker S ^a  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

3 HYDROXYGLUTARIC ACID; CARNITINE; ESSENTIAL AMINO ACID; GLUTARIC ACID; GLUTARIC ACID DERIVATIVE; GLUTARYL COENZYME A DEHYDROGENASE; LYSINE; TRACE ELEMENT; TRYPTOPHAN; UNCLASSIFIED DRUG;

AGE DISTRIBUTION; AMINO ACID METABOLISM; ARTICLE; BRAIN DISEASE; DIET RESTRICTION; DIET SUPPLEMENTATION; DIETARY INTAKE; ENZYME DEFICIENCY; FOOD COMPOSITION; FREQUENCY ANALYSIS; HUMAN; INBORN ERROR OF METABOLISM; INFANT; MALNUTRITION; MILK; NUTRITIONAL SUPPORT; PRESCHOOL CHILD; PROSPECTIVE STUDY; PROTEIN INTAKE; PROTEIN RESTRICTION; RELIABILITY; RISK BENEFIT ANALYSIS; RISK REDUCTION; TREATMENT OUTCOME;

ADULT; AGING; AMINO ACID METABOLISM, INBORN ERRORS; CHILD; CHILD, PRESCHOOL; DIET, PROTEIN-RESTRICTED; GLUTARYL-COA DEHYDROGENASE; HUMANS; INFANT; LYSINE; MALNUTRITION; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS;

EID: 7244251623     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/B:BOLI.0000045775.03183.48     Document Type: Article

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