Arrhythmogenic right ventricular cardiomyopathy plakophilin-2 Mutations Disrupt desmosome assembly and stability

Cell Communication and Adhesion

Volumn 16, Issue 1-3, 2009, Pages 15-27

  Hall, Chad ^a   Li, Shumin ^a   Li, Hong ^a   Creason, Valeta ^a   Wahl III, James K ^a  

^a UNIVERSITY OF NEBRASKA MEDICAL CENTER   (United States)

Author keywords

ARVC; Desmosome; Plakophilin 2

Indexed keywords

DESMOPLAKIN; GLUTATHIONE TRANSFERASE; NERVE CELL ADHESION MOLECULE; PLAKOPHILIN; PROTEIN PLAKOPHILIN 2; UNCLASSIFIED DRUG; UVOMORULIN;

ARTICLE; CELL CONTACT; CELL CULTURE; CELL LINE; CONTROLLED STUDY; DESMOSOME; EPITHELIUM CELL; HEART MUSCLE CELL; HEART RIGHT VENTRICLE DYSPLASIA; HUMAN; HUMAN CELL; INTERMEDIATE FILAMENT; MECHANICAL STRESS; MOLECULAR INTERACTION; MUTATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN INTERACTION;

AMINO ACID SEQUENCE; AMINO ACID SUBSTITUTION; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; CELL LINE, TUMOR; DESMOPLAKINS; DESMOSOMES; EPITHELIAL CELLS; HUMANS; MOLECULAR SEQUENCE DATA; MUTAGENESIS, SITE-DIRECTED; PLAKOPHILINS; PROTEIN STRUCTURE, TERTIARY; RECOMBINANT FUSION PROTEINS; SEQUENCE DELETION;

EID: 72149099859     PISSN: 15419061     EISSN: 15435180     Source Type: Journal    
DOI: 10.1080/15419060903009329     Document Type: Article

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