Progressive familial intrahepatic cholestasis presenting as liver failure;Fallo hepático neonatal como forma de presentación de colestasis intrahepática familiar progresiva

Anales de Pediatria

Volumn 71, Issue 6, 2009, Pages 510-513

  Sangorrin Iranzo, A ^a   Iriondo Sanz, M ^a   Alvarez Garcia L ^b   Jara Vega, P ^b   Martin De Carpi J ^a  

^a HOSPITAL SANT JOAN DE DÉU   (Spain)

^b HOSPITAL INFANTIL LA PAZ   (Spain)

Author keywords

Bile salt export pump; Liver failure; Neonatal cholestasis; Progressive familial intrahepatic cholestasis

Indexed keywords

ARTICLE; CASE REPORT; CHILD; ECHOCARDIOGRAPHY; HUMAN; IMMUNOHISTOCHEMISTRY; INTRAHEPATIC CHOLESTASIS; LIVER BIOPSY; LIVER FAILURE; LIVER FUNCTION TEST; PRESCHOOL CHILD; PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS;

CHOLESTASIS, INTRAHEPATIC; DISEASE PROGRESSION; HUMANS; INFANT, NEWBORN; LIVER FAILURE; MALE;

EID: 70450274938     PISSN: 16954033     EISSN: 16959531     Source Type: Journal    
DOI: 10.1016/j.anpedi.2009.08.005     Document Type: Article

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