Polyethylene glycol-modified adenosine deaminase improved lung disease but not liver disease in partial adenosine deaminase deficiency

Journal of Allergy and Clinical Immunology

Volumn 124, Issue 4, 2009, Pages 848-850

  Somech, Raz ^a,b   Lai, Yew Hon ^a,b   Grunebaum, Eyal ^a,b   Le Saux, Nicole ^c   Cutz, Ernest ^b,d   Roifman, Chaim M ^a,b  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^c CHILDREN S HOSPITAL OF EASTERN ONTARIO   (Canada)

^d NONE

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE DEAMINASE; ALANINE; ALANINE AMINOTRANSFERASE; ANTIINFECTIVE AGENT; CD19 ANTIGEN; CD2 ANTIGEN; CD56 ANTIGEN; CD68 ANTIGEN; CYSTEINE; GENOMIC DNA; GLUTAMINE; GLYCINE; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; LIVE VACCINE; METHIONINE; MICROSOME ANTIBODY; MITOGENIC AGENT; PEGADEMASE; PREDNISONE; PROTEIN GLUTAMINE GAMMA GLUTAMYLTRANSFERASE ANTIBODY; T LYMPHOCYTE RECEPTOR; THREONINE; VALINE; IMMUNOGLOBULIN; PEGADEMASE BOVINE;

ADENOSINE DEAMINASE DEFICIENCY; ALANINE AMINOTRANSFERASE BLOOD LEVEL; AMINO ACID SUBSTITUTION; ANTIBODY TITER; ANTIMICROBIAL THERAPY; B LYMPHOCYTE; BACTEREMIA; CASE REPORT; CD3+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELL HYPERPLASIA; CERVICAL LYMPH NODE; CHILD; CODON; COUGHING; DBA 1 MOUSE; DNA SEQUENCE; ECHOGRAPHY; ELECTRON MICROSCOPY; ENZYME BLOOD LEVEL; ENZYME THERAPY; EOSINOPHIL; EXON; FLOW CYTOMETRY; GOBLET CELL; HEPATITIS; HERPES SIMPLEX; HERPES SIMPLEX VIRUS 1; HISTIOCYTE; HUMAN; HUMAN TISSUE; HYPOXIA; IMMUNE DEFICIENCY; IMMUNIZATION; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOHISTOCHEMISTRY; IMMUNOSUPPRESSIVE TREATMENT; INFANT; INFLAMMATORY INFILTRATE; INGUINAL LYMPH NODE; LETTER; LIVER BIOPSY; LIVER FIBROSIS; LUNG BIOPSY; LYMPHOCYTE; MACROPHAGE; MALE; MAST CELL; MISSENSE MUTATION; MOUTH ULCER; NATURAL KILLER CELL; OXYGEN THERAPY; PERIANAL ABSCESS; PLASMA CELL; PNEUMOCOCCAL INFECTION; PNEUMONIA; PORTAL VEIN; PRESCHOOL CHILD; PRIORITY JOURNAL; SINUSITIS; SOMALIA; STOP CODON; STREPTOCOCCUS PNEUMONIAE; SURGICAL DRAINAGE; TACHYPNEA; THORAX RADIOGRAPHY; THYMUS; TONSIL; VIRUS PARTICLE; BLOOD; ENZYMOLOGY; ERYTHROCYTE; FOLLOW UP; LIVER DISEASE; LUNG DISEASE; METABOLISM; NEWBORN; SEVERE COMBINED IMMUNODEFICIENCY;

ADENOSINE DEAMINASE; ERYTHROCYTES; FOLLOW-UP STUDIES; HUMANS; IMMUNOGLOBULINS; INFANT, NEWBORN; LIVER DISEASES; LUNG DISEASES; LYMPHOCYTES; MALE; SEVERE COMBINED IMMUNODEFICIENCY;

EID: 70449704186     PISSN: 00916749     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jaci.2009.07.003     Document Type: Letter

References (9)

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