Evaluation of the therapeutic potential of carbonic anhydrase inhibitors in two animal models of dystrophin deficient muscular dystrophy

Human Molecular Genetics

Volumn 18, Issue 21, 2009, Pages 4089-4101

  Giacomotto, Jean ^a   Pertl, Cordula ^b   Borrel, Caroline ^a   Walter, Maggie C ^b   Bulst, Stefanie ^b   Johnsen, Bob ^c   Baillie, David L ^c   Lochmüller, Hanns ^d   Thirion, Christian ^b   Ségalat, Laurent ^a  

^a CENTRE DE GÉNÉTIQUE MOLÉCULAIRE ET CELLULAIRE   (France)

^b LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

^c SIMON FRASER UNIVERSITY   (Canada)

^d NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

CARBONATE DEHYDRATASE INHIBITOR; CARBONATE DEHYDRATASE IV; DICLOFENAMIDE; DOUBLE STRANDED RNA; DYSTROPHIN; METHAZOLAMIDE; SULFONAMIDE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CAENORHABDITIS ELEGANS; CONCENTRATION RESPONSE; CONTROLLED STUDY; DIAPHRAGM; DOSE RESPONSE; DRUG EFFICACY; DRUG MECHANISM; DRUG MEGADOSE; DRUG POTENTIATION; DRUG SCREENING; DUCHENNE MUSCULAR DYSTROPHY; ECCENTRIC MUSCLE CONTRACTION; ENZYME INHIBITION; EXTENSOR DIGITORUM LONGUS MUSCLE; HISTOPATHOLOGY; LOW DRUG DOSE; MOUSE; MUSCLE FORCE; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; RNA INTERFERENCE; TIBIALIS ANTERIOR MUSCLE; TISSUE DISTRIBUTION; VALIDATION PROCESS; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ANIMALIA; CAENORHABDITIS ELEGANS; MUS;

EID: 70349993595     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddp358     Document Type: Article

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