A blue baby grows up

Congenital Heart Disease

Volumn 4, Issue 5, 2009, Pages 378-383

  Aboulhosn, Jamil A ^a   Child, John S ^a  

^a UCLA MEDICAL CENTER   (United States)

Author keywords

Adult; Congenital heart Disease; Cyanosis; Pulmonary hypertension; Single ventricle; Tricuspid atresia

Indexed keywords

BOSENTAN; SILDENAFIL;

ADULT; ARTICLE; CASE REPORT; CYANOSIS; CYANOTIC HEART DISEASE; FEMALE; GREAT VESSELS TRANSPOSITION; HEART ATRIUM SEPTUM DEFECT; HEART CATHETERIZATION; HEART RIGHT VENTRICLE DYSPLASIA; HUMAN; LUNG ARTERY BANDING; PRIORITY JOURNAL; PULMONARY HYPERTENSION; TRICUSPID VALVE ATRESIA; UPPER RESPIRATORY TRACT INFECTION; WEIGHT GAIN;

ABNORMALITIES, MULTIPLE; ADULT; ANTI-ARRHYTHMIA AGENTS; ANTIHYPERTENSIVE AGENTS; ARRHYTHMIAS, CARDIAC; CARDIAC SURGICAL PROCEDURES; CYANOSIS; DISEASE PROGRESSION; FEMALE; HEART CATHETERIZATION; HEART DEFECTS, CONGENITAL; HEMODYNAMICS; HUMANS; HYPERTENSION, PULMONARY; INFANT, NEWBORN; MAGNETIC RESONANCE IMAGING, CINE; PALLIATIVE CARE; PREGNANCY; PREGNANCY COMPLICATIONS, CARDIOVASCULAR; TREATMENT OUTCOME;

EID: 70149088391     PISSN: 1747079X     EISSN: 17470803     Source Type: Journal    
DOI: 10.1111/j.1747-0803.2009.00276.x     Document Type: Article

References (21)

1. Marelli AJ, Mackie AS, Ionescu-Ittu R, Rahme E, Pilote L. Congenital heart disease in the general population: Changing prevalence and age distribution. Circulation. 2007;115:163-172.
2. Dick M, Fyler DC, Nadas AS. Tricuspid atresia: Clinical course in 101 patients. Am J Cardiol. 1975;36:327-337.
3. Kaemmerer H, Bauer U, Pensl U, et al. Management of emergencies in adults with congenital cardiac disease. Am J Cardiol. 2008;101:521-525.
4. Walsh EP. Arrhythmias in patients with congenital heart disease. Card Electrophysiol Rev. 2002;6:422-430.
5. Gatzoulis MA, Freeman MA, Siu SC, Webb GD, Harris L. Atrial arrhythmia after surgical closure of atrial septal defects in adults. N Engl J Med. 1999;340:839-846.
6. Lan YT, Chang RK, Laks H. Outcome of patients with double-inlet left ventricle or tricuspid atresia with transposed great arteries. J Am Coll Cardiol. 2004;43:113-119.
7. Pinho P, Von Oppell UO, Brink J, Hewitson J. Pulmonary artery banding: adequacy and long-term outcome. Eur J Cardiothorac Surg. 1997;11:105-111.
8. Presbitero P, Somerville J, Stone S, Aruta E, Spiegelhalter D, Rabajoli F. Pregnancy in cyanotic congenital heart disease. Outcome of mother and fetus. Circulation. 1994;89:2673-2676.
9. Siu SC, Sermer M, Harrison DA, et al. Risk and predictors for pregnancy-related complications in women with heart disease. Circulation. 1997;96:2789-2794.
10. Khairy P, Ouyang DW, Fernandes SM, Lee-Parritz A, Economy KE, Landzberg MJ. Pregnancy outcomes in women with congenital heart disease. Circulation. 2006;113:517-524.
11. Galie N, Torbicki A, Barst R, etal. Guidelines on diagnosis and treatment of pulmonary arterial hypertension. The task force on diagnosis and treatment of pulmonary arterial hypertension of the European Society of Cardiology. Eur Heart J. 2004;25:2243-2278.
12. Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. Br Med J. 1958;2:755-762.
13. Galie N, Beghetti M, Gatzoulis MA, et al. Bosentan therapy in patients with Eisenmenger syndrome: A multicenter, double-blind, randomized, placebo-controlled study. Circulation. 2006;114:48-54.
14. Gatzoulis MA, Beghetti M, Galie N, etal. Longer-term bosentan therapy improves functional capacity in Eisenmenger syndrome: Results of the BREATHE-5 open-label extension study. Int J Cardiol. 2007;127:27-32.
15. Apostolopoulou SC, Manginas A, Cokkinos DV, Rammos S. Long-term oral bosentan treatment in patients with pulmonary arterial hypertension related to congenital heart disease: A 2-year study. Heart. 2007;93:350-354.
16. Schulze-Neick I, Hartenstein P, Li J, etal. Intravenous sildenafil is a potent pulmonary vasodilator in children with congenital heart disease. Circulation. 2003;108(Suppl 1):II167-173.
17. Okyay K, Cemri M, Boyac B, Yalcn R, Cengel A. Use of long-term combined therapy with inhaled iloprost and oral sildenafil in an adult patient with Eisenmenger syndrome. Cardiol Rev. 2005;13:312-314.
18. Mukhopadhyay S, Sharma M, Ramakrishnan S, et al. Phosphodiesterase-5 inhibitor in Eisenmenger syndrome: A preliminary observational study. Circulation. 2006;114:1807-1810.
19. Lunze K, Gilbert N, Mebus S, etal. First experience with an oral combination therapy using bosentan and sildenafil for pulmonary arterial hypertension. Eur J Clin Invest. 2006;36:32-38.
20. Ivy DD, Doran AK, Smith KJ, et al. Short- and long-term effects of inhaled iloprost therapy in children with pulmonary arterial hypertension. J Am Coll Cardiol. 2008;51:161-169.
21. Batista RJ, Santos JL, Takeshita N, etal. Successful reversal of pulmonary hypertension in Eisenmenger complex. Arq Bras Cardiol. 1997;68:279-280.