메뉴 건너뛰기




Volumn 66, Issue 8, 2009, Pages 931-932

Drilling for energy in mitochondrial disease

Author keywords

[No Author keywords available]

Indexed keywords

ASCORBIC ACID; BEZAFIBRATE; DICHLOROACETIC ACID; MENADIONE; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR AGONIST; RIBOFLAVIN; SUCCINIC ACID; UBIDECARENONE;

EID: 68549130877     PISSN: 00039942     EISSN: 15383687     Source Type: Journal    
DOI: 10.1001/archneurol.2009.155     Document Type: Editorial
Times cited : (5)

References (16)
  • 1
    • 48249156188 scopus 로고    scopus 로고
    • Mitochondrial disorders in the nervous system
    • DiMauro S, Schon EA. Mitochondrial disorders in the nervous system. Annu Rev Neurosci. 2008;31:91-123.
    • (2008) Annu Rev Neurosci , vol.31 , pp. 91-123
    • DiMauro, S.1    Schon, E.A.2
  • 2
    • 57049143140 scopus 로고    scopus 로고
    • Mitochondria in neuroplasticity and neurological disorders
    • Mattson MP, Gleichmann M, Cheng A. Mitochondria in neuroplasticity and neurological disorders. Neuron. 2008;60(5):748-766.
    • (2008) Neuron , vol.60 , Issue.5 , pp. 748-766
    • Mattson, M.P.1    Gleichmann, M.2    Cheng, A.3
  • 3
    • 58149349815 scopus 로고    scopus 로고
    • Mitochondrial medicine: Entering the era of treatment
    • Koene S, Smeitink J. Mitochondrial medicine: entering the era of treatment. J Intern Med. 2009;265(2):193-209.
    • (2009) J Intern Med , vol.265 , Issue.2 , pp. 193-209
    • Koene, S.1    Smeitink, J.2
  • 4
    • 34250676955 scopus 로고    scopus 로고
    • Mitochondrial diseases: Therapeutic approaches
    • DiMauro S, Mancuso M. Mitochondrial diseases: therapeutic approaches. Biosci Rep. 2007;27(1-3):125-137.
    • (2007) Biosci Rep , vol.27 , Issue.1-3 , pp. 125-137
    • DiMauro, S.1    Mancuso, M.2
  • 5
    • 20444392739 scopus 로고    scopus 로고
    • Interactions of mitochondriatargeted and untargeted ubiquinones with the mitochondrial respiratory chain and reactive oxygen species: Implications for the use of exogenous ubiquinones as therapies and experimental tools
    • James AM, Cocheme HM, Smith RA, Murphy MP. Interactions of mitochondriatargeted and untargeted ubiquinones with the mitochondrial respiratory chain and reactive oxygen species: implications for the use of exogenous ubiquinones as therapies and experimental tools. J Biol Chem. 2005;280(22):21295-21312.
    • (2005) J Biol Chem , vol.280 , Issue.22 , pp. 21295-21312
    • James, A.M.1    Cocheme, H.M.2    Smith, R.A.3    Murphy, M.P.4
  • 6
    • 0021449807 scopus 로고
    • 31P NMR study of improvement in oxidative phosphorylation by vitamins K3 and C in a patient with a defect in electron transport at complex III in skeletal muscle
    • Eleff S, Kennaway NG, Buist NR, et al. 31P NMR study of improvement in oxidative phosphorylation by vitamins K3 and C in a patient with a defect in electron transport at complex III in skeletal muscle. Proc Natl Acad Sci U S A. 1984; 81(11):3529-3533.
    • (1984) Proc Natl Acad Sci U S A , vol.81 , Issue.11 , pp. 3529-3533
    • Eleff, S.1    Kennaway, N.G.2    Buist, N.R.3
  • 7
    • 51249120293 scopus 로고    scopus 로고
    • The mitochondrial cocktail: Rationale for combined nutraceutical therapy in mitochondrial cytopathies
    • Tarnopolsky MA. The mitochondrial cocktail: rationale for combined nutraceutical therapy in mitochondrial cytopathies. Adv Drug Deliv Rev. 2008;60(13-14): 1561-1567.
    • (2008) Adv Drug Deliv Rev , vol.60 , Issue.13-14 , pp. 1561-1567
    • Tarnopolsky, M.A.1
  • 8
    • 33845285545 scopus 로고    scopus 로고
    • Endurance training and detraining in mitochondrial myopathies due to single large-scale mtDNA deletions
    • Taivassalo T, Gardner JL, Taylor RW, et al. Endurance training and detraining in mitochondrial myopathies due to single large-scale mtDNA deletions. Brain. 2006; 129(Pt 12):3391-3401.
    • (2006) Brain , vol.129 , Issue.PART 12 , pp. 3391-3401
    • Taivassalo, T.1    Gardner, J.L.2    Taylor, R.W.3
  • 9
    • 33845288002 scopus 로고    scopus 로고
    • Aerobic training is safe and improves exercise capacity in patients with mitochondrial myopathy
    • Jeppesen TD, Schwartz M, Olsen DB, et al. Aerobic training is safe and improves exercise capacity in patients with mitochondrial myopathy. Brain. 2006;129 (pt 12):3402-3412.
    • (2006) Brain , vol.129 , Issue.PART 12 , pp. 3402-3412
    • Jeppesen, T.D.1    Schwartz, M.2    Olsen, D.B.3
  • 10
    • 48449094498 scopus 로고    scopus 로고
    • AMPK and PPARδ agonists are exercise mimetics
    • Narkar VA, Downes M, Yu RT, et al. AMPK and PPARδ agonists are exercise mimetics. Cell. 2008;134(3):405-415.
    • (2008) Cell , vol.134 , Issue.3 , pp. 405-415
    • Narkar, V.A.1    Downes, M.2    Yu, R.T.3
  • 11
    • 50049118173 scopus 로고    scopus 로고
    • Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype
    • Wenz T, Diaz F, Spiegelman BM, Moraes CT. Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype. Cell Metab. 2008;8(3):249-256.
    • (2008) Cell Metab , vol.8 , Issue.3 , pp. 249-256
    • Wenz, T.1    Diaz, F.2    Spiegelman, B.M.3    Moraes, C.T.4
  • 12
    • 60849099038 scopus 로고    scopus 로고
    • Bezafibrate for an inborn mitochondrial beta-oxidation defect
    • Bonnefont JP, Bastin J, Behin A, Djouadi F. Bezafibrate for an inborn mitochondrial beta-oxidation defect. N Engl J Med. 2009;360(8):838-840.
    • (2009) N Engl J Med , vol.360 , Issue.8 , pp. 838-840
    • Bonnefont, J.P.1    Bastin, J.2    Behin, A.3    Djouadi, F.4
  • 13
    • 0035003001 scopus 로고    scopus 로고
    • Exercise intolerance in mitochondrial myopathy is not related to lactic acidosis
    • Vissing J, Gansted U, Quistorff B. Exercise intolerance in mitochondrial myopathy is not related to lactic acidosis. Ann Neurol. 2001;49(5):672-676.
    • (2001) Ann Neurol , vol.49 , Issue.5 , pp. 672-676
    • Vissing, J.1    Gansted, U.2    Quistorff, B.3
  • 14
    • 33646202306 scopus 로고    scopus 로고
    • Dichloroacetate causes toxic neuropathy in MELAS: A randomized, controlled clinical trial
    • Kaufmann P, Engelstad K, Wei Y, et al. Dichloroacetate causes toxic neuropathy in MELAS: a randomized, controlled clinical trial. Neurology. 2006;66(3):324-330.
    • (2006) Neurology , vol.66 , Issue.3 , pp. 324-330
    • Kaufmann, P.1    Engelstad, K.2    Wei, Y.3
  • 15
    • 68549110570 scopus 로고    scopus 로고
    • Human NARP mitochondrial mutation metabolism corrected with α-ketoglutarate/ aspartate: A potential new therapy
    • Sgarbi G, Casalena GA, Baracca A, Lenaz G, DiMauro S, Solaini G. Human NARP mitochondrial mutation metabolism corrected with α-ketoglutarate/ aspartate: a potential new therapy. Arch Neurol. 2009;66(8):951-957.
    • (2009) Arch Neurol , vol.66 , Issue.8 , pp. 951-957
    • Sgarbi, G.1    Casalena, G.A.2    Baracca, A.3    Lenaz, G.4    DiMauro, S.5    Solaini, G.6
  • 16
    • 4344718634 scopus 로고    scopus 로고
    • Expression of two succinyl-CoA synthetases with different nucleotide specificities in mammalian tissues
    • Lambeth DO, Tews KN, Adkins S, Frohlich D, Milavetz BI. Expression of two succinyl-CoA synthetases with different nucleotide specificities in mammalian tissues.JBiol Chem. 2004;279(35):36621-36624.
    • (2004) JBiol Chem , vol.279 , Issue.35 , pp. 36621-36624
    • Lambeth, D.O.1    Tews, K.N.2    Adkins, S.3    Frohlich, D.4    Milavetz, B.I.5


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.