Bleeding in the heritable connective tissue disorders: Mechanisms, diagnosis and treatment

Blood Reviews

Volumn 23, Issue 5, 2009, Pages 191-197

  Malfait, Fransiska ^a   Paepe, Anne De ^a  

^a GHENT UNIVERSITY HOSPITAL   (Belgium)

Author keywords

Bleeding tendency; Diagnosis; Easy bruising; Ehlers Danlos syndrome; Heritable disorders of connective tissue; Management

Indexed keywords

ASCORBIC ACID; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; COLLAGEN TYPE 1; COLLAGEN TYPE 11; COLLAGEN TYPE 2; COLLAGEN TYPE 3; COLLAGEN TYPE 5; DESMOPRESSIN; FIBRILLIN 1; RECOMBINANT BLOOD CLOTTING FACTOR 7A;

ARTICLE; BLEEDING TENDENCY; CAPILLARY RESISTANCE; CLINICAL FEATURE; DIAGNOSTIC VALUE; DIFFERENTIAL DIAGNOSIS; DISEASE CLASSIFICATION; DRUG EFFICACY; EHLERS DANLOS SYNDROME; FATALITY; GENE MUTATION; HEMOPHILIA; HEMOSTASIS; HEREDITARY CONNECTIVE TISSUE DISEASE; HUMAN; JOINT HYPERMOBILITY; MARFAN SYNDROME; PRIMARY PREVENTION; PRIORITY JOURNAL; PROTECTIVE CLOTHING; SKIN FRAGILITY; VASCULAR FRAGILITY; VON WILLEBRAND DISEASE;

COLLAGEN TYPE III; CONNECTIVE TISSUE DISEASES; DEAMINO ARGININE VASOPRESSIN; EHLERS-DANLOS SYNDROME; EXTRACELLULAR MATRIX; HEMORRHAGE; HEMOSTASIS; HEMOSTATICS; HUMANS;

EID: 68349135410     PISSN: 0268960X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.blre.2009.06.001     Document Type: Article

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