Steroid pulse therapy for protein-losing enteropathy after the Fontan operation

Congenital Heart Disease

Volumn 4, Issue 4, 2009, Pages 284-287

  Hoashi, Takaya ^a   Ichikawa, Hajime ^a   Ueno, Takayoshi ^a   Kogaki, Shigetoyo ^a   Sawa, Yoshiki ^a  

^a OSAKA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Fontan; Protein losing enteropathy; Steroid pulse therapy

Indexed keywords

ALBUMIN; C REACTIVE PROTEIN; CEFMETAZOLE; DIURETIC AGENT; HEPARIN; IMMUNOGLOBULIN; METHYLPREDNISOLONE; PLASMA PROTEIN; PREDNISOLONE;

ADULT; ALBUMIN BLOOD LEVEL; ANAMNESIS; ARTICLE; ASCITES; BONE MARROW SUPPRESSION; CASE REPORT; CLINICAL FEATURE; DRUG DOSE REDUCTION; DRUG EFFICACY; DRUG MEGADOSE; DRUG PULSE THERAPY; DRUG WITHDRAWAL; ECHOGRAPHY; ENTERITIS; FONTAN PROCEDURE; HEART ATRIUM SEPTUM DEFECT; HUMAN; INFLAMMATION; MALE; POSTOPERATIVE COMPLICATION; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN LOSING GASTROENTEROPATHY; STEROID THERAPY; THROMBOCYTOPENIA; TREATMENT DURATION; TREATMENT RESPONSE;

ADMINISTRATION, ORAL; FONTAN PROCEDURE; GLUCOCORTICOIDS; HUMANS; INJECTIONS, INTRAVENOUS; MALE; METHYLPREDNISOLONE; POSTOPERATIVE COMPLICATIONS; PROTEIN-LOSING ENTEROPATHIES; PULSE THERAPY, DRUG; TECHNETIUM TC 99M AGGREGATED ALBUMIN; YOUNG ADULT;

EID: 68249138376     PISSN: 1747079X     EISSN: 17470803     Source Type: Journal    
DOI: 10.1111/j.1747-0803.2009.00274.x     Document Type: Article

References (16)

1. Feldt RH, Driscoll DJ, Offord KP, et al. Protein-losing enteropathy after the Fontan operation. J Thorac Cardiovasc Surg. 1996;112:672-680.
2. Mertens L, Hagler DJ, Sauer U, Somerville J, Gewillig M. Protein-losing enteropathy after the Fontan operation: An international multicenter study. PLE study group. J Thorac Cardiovasc Surg. 1998;115:1063-1073.
3. Ostrow AM, Freeze H, Rychik J. Protein-losing enteropathy after fontan operation: Investigations into possible pathophysiologic mechanisms. Ann Thorac Surg. 2006;82:695-701.
4. Shimizu T, Nagata S, Fujii T, et al. Enhanced production of interferon-gamma as a possible cause of protein-losing enteropathy after modified Fontan operation. J Pediatr Gastroenterol Nutr. 2003;37:504-507.
5. Powell AJ, Gauvreau K, Jenkins KJ, Blume ED, Mayer JE, Lock JE. Perioperative risk factors for development of protein-losing enteropathy following a Fontan procedure. Am J Cardiol. 2001;88:1206-1209.
6. Rothman A, Snyder J. Protein-losing enteropathy following the Fontan operation: Resolution with prednisone therapy. Am Heart J. 1991;121:618-619.
7. Therrien J, Webb GD, Gatzoulis MA. Reversal of protein losing enteropathy with prednisone in adults with modified fontan operations: long term palliation or bridge to cardiac transplantation? Heart. 1999;82:241-243.
8. Zellers TM, Brown K. Protein-losing enteropathy after the modified fontan operation: Oral predonisone treatment with biopsy and laboratory proved improvement. Pediatr Cardiol. 1996;17:115-117.
9. Rychik J, Piccoli DA, Barber G. Usefulness of corticosteroid therapy for protein-losing enteropathy after the Fontan procedure. Am J Cardiol. 1991;68:819-821.
10. Donnelly JP, Rosenthal A, Castle VP, Holmes RD. Reversal of protein-losing enteropathy with heparin therapy in three patients with univentricular hearts and Fontan palliation. J Pediatr. 1997;130:474-478.
11. Ryerson L, Goldberg C, Rosenthal A, Armstrong A. Usefulness of heparin therapy in protein-losing enteropathy associated with single ventricle palliation. Am J Cardiol. 2008;101:248-251.
12. Ringel RE, Peddy SB. Effect of high-dose spironolactone on protein-losing enteropathy in patients with Fontan palliation of complex congenital heart disease. Am J Cardiol. 2003;91:1031-1032.
13. Kim SJ, Park IS, Song JY, Lee JY, Shim WS. Reversal of protein-losing enteropathy with calcium replacement in a patient after Fontan operation. Ann Thorac Surg. 2004;77:1456-1457.
14. Bernstein D, Naftel D, Chin C, et al. Outcome of listing for cardiac transplantation for failed Fontan: A multi-institutional study. Circulation. 2006;114:273-280.
15. Gamba A, Merlo M, Fiocchi R, et al. Heart transplantation in patients with previous Fontan operations. J Thorac Cardiovasc Surg. 2004;127:555-562.
16. Lenz D, Hambsch J, Schneider P, et al. Protein-losing enteropathy in patients with Fontan circulation: Is it triggered by infection? Crit Care. 2003;7:185-190.