Osmotic demyelination syndrome as a consequence of treating hyperammonemia in a patient with ornithine transcarbamylase deficiency

Journal of Child Neurology

Volumn 24, Issue 7, 2009, Pages 884-886

  Cardenas, Javier F ^a,b   Bodensteiner, John B ^a  

^a BARROW NEUROLOGICAL INSTITUTE   (United States)

^b NONE   (United States)

Author keywords

Hyperammonemia; Osmotic demyelination; Urea cycle defect

Indexed keywords

AGENTS AFFECTING METABOLISM; ALANINE; ALANINE AMINOTRANSFERASE; AMMONIA; ASPARTATE AMINOTRANSFERASE; BENZOIC ACID; GLUTAMINE; ORNITHINE CARBAMOYLTRANSFERASE; PHENYLACETATE SODIUM; STEROID; UNCLASSIFIED DRUG;

AGITATION; ALANINE AMINOTRANSFERASE BLOOD LEVEL; AMINO ACID BLOOD LEVEL; AMMONIA BLOOD LEVEL; APRAXIA; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; ATAXIA; CASE REPORT; CENTRAL PONTINE MYELINOLYSIS; CHILD; CONFUSION; DEMYELINATING DISEASE; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; DYSARTHRIA; DYSMETRIA; FEMALE; GAIT DISORDER; HALLUCINATION; HUMAN; HYPERAMMONEMIA; LABORATORY DIAGNOSIS; MUSCLE SPASM; NEUROIMAGING; NEUROLOGIC EXAMINATION; NUCLEAR MAGNETIC RESONANCE IMAGING; OSMOTIC DEMYELINATION SYNDROME; PRIORITY JOURNAL; PROTEIN INTAKE; SCHOOL CHILD; WHITE MATTER;

BRAIN; CHILD; DEMYELINATING DISEASES; FEMALE; HUMANS; HYPERAMMONEMIA; MAGNETIC RESONANCE IMAGING; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; STEROIDS; SYNDROME; TREATMENT OUTCOME;

EID: 67949115726     PISSN: 08830738     EISSN: None     Source Type: Journal    
DOI: 10.1177/0883073808331349     Document Type: Article

References (13)

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