Idiopathic pulmonary arterial hypertension in a patient with pyruvate kinase deficiency and paravertebral extramedullary hematopoiesis

Annals of Hematology

Volumn 88, Issue 6, 2009, Pages 603-605

  Bachmeyer, C ^a   Khalil, A ^a   Kerrou, K ^a   Girot, R ^a   Gounant, V ^a  

^a HÔPITAL TENON   (France)

Author keywords

[No Author keywords available]

Indexed keywords

PYRUVATE KINASE;

ADULT; ANAMNESIS; ARTERIAL CARBON DIOXIDE TENSION; ARTERIAL GAS; ARTERIAL OXYGEN TENSION; ASPIRATION BIOPSY; CASE REPORT; DISEASE ASSOCIATION; ECHOCARDIOGRAPHY; ENZYME DEFICIENCY; EXTRAMEDULLARY HEMATOPOIESIS; HEART CATHETERIZATION; HEART LEFT VENTRICLE HYPERTROPHY; HUMAN; IDIOPATHIC DISEASE; JAUNDICE; LETTER; LUNG FUNCTION TEST; LUNG SCINTISCANNING; LUNG WEDGE PRESSURE; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; OXYGEN SATURATION; PRIORITY JOURNAL; PULMONARY HYPERTENSION; SYSTOLIC HEART MURMUR; TRICUSPID VALVE REGURGITATION; WHOLE BODY SCINTISCANNING; BLOOD; ENZYMOLOGY; METABOLISM; MIDDLE AGED; PATHOLOGY; RADIOGRAPHY;

HEMATOPOIESIS, EXTRAMEDULLARY; HUMANS; HYPERTENSION, PULMONARY; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; PYRUVATE KINASE;

EID: 67651053275     PISSN: 09395555     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00277-008-0644-z     Document Type: Letter

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