Excessive erythrocyte ppix influences the hematologic status and iron metabolism in patients with dominant erythropoietic protoporphyria

Cellular and Molecular Biology

Volumn 55, Issue 1, 2009, Pages 45-52

  Delaby, C ^a,b,c,d   Lyoumi, S ^a,b   Ducamp, S ^a,b   Martin Schmitt, C ^a,b   Gouya, L ^a,b,c,d   Deybach, J C ^a,b,c,d   Beaumont, C ^a,b   Puy, Hervé ^a,b,c,d  

^a CENTRE DE RECHERCHE BIOMÉDICALE BICHAT BEAUJON CRB3   (France)

^b LABORATOIRE DES SCIENCES DU CLIMAT ET DE L ENVIRONNEMENT   (France)

^c HÔPITAL LOUIS MOURIER   (France)

^d HÔPITAL AMBROISE PARÉ   (France)

Author keywords

Erythropo etic protoporphyria; Ferrochelatase; Liver; Protoporphyrin IX

Indexed keywords

ERYTHROCYTE PROTOPORPHYRIN; ERYTHROCYTE PROTOPORPHYRIN 9; FERROCHELATASE; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AMINO ACID ANALYSIS; ANEMIA; ARTICLE; CHILD; CONTROLLED STUDY; ENZYME ACTIVITY; ERYTHROPOIESIS; ERYTHROPOIETIC PROTOPORPHYRIA; FEMALE; HUMAN; IRON BLOOD LEVEL; IRON METABOLISM; LIVER METABOLISM; MAJOR CLINICAL STUDY; MALE; SCHOOL CHILD; THROMBOCYTOPENIA;

ADOLESCENT; ADULT; CHILD; ERYTHROCYTES; ERYTHROPOIESIS; FEMALE; HUMANS; IRON; LIPIDS; LIVER FUNCTION TESTS; MALE; MIDDLE AGED; PORPHYRINS; PROTOPORPHYRIA, ERYTHROPOIETIC; PROTOPORPHYRINS; YOUNG ADULT;

EID: 67449164823     PISSN: 01455680     EISSN: 1165158X     Source Type: Journal    
DOI: 10.1170/T837     Document Type: Article

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