Severe hemolysis and methemoglobinemia following fava beans ingestion in glucose-6-phosphatase dehydrogenase deficiency-case report and literature review

European Journal of Pediatrics

Volumn 168, Issue 7, 2009, Pages 779-782

  Schuurman, Marijn ^a   Van Waardenburg, Dick ^b   Costa, Joost Da ^a   Niemarkt, Hendrik ^a   Leroy, Piet ^b  

^a Sittard Geleen Heerlen   (Netherlands)

^b MAASTRICHT UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Acute hemolysis; Child; Favism; Glucose 6 phospate dehydrogenase deficiency; Methemoglobinemia

Indexed keywords

FUROSEMIDE; GLUCOSE 6 PHOSPHATE DEHYDROGENASE; METHEMOGLOBIN;

ACUTE KIDNEY FAILURE; ALKALINIZATION; CASE REPORT; CHILD; CYANOSIS; DISEASE SEVERITY; ERYTHROCYTE TRANSFUSION; FAVISM; FEVER; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY; HEMODYNAMIC PARAMETERS; HEMOLYTIC ANEMIA; HUMAN; INFANT; INGESTION; IRRITABILITY; MALAISE; MALE; METHEMOGLOBINEMIA; OUTCOME ASSESSMENT; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PRESCHOOL CHILD; PRIORITY JOURNAL; REVIEW; VICIA FABA;

CYANOSIS; FAVISM; GLYCOGEN STORAGE DISEASE TYPE I; HEMOLYSIS; HUMANS; INFANT; KIDNEY FAILURE, ACUTE; MALE; METHEMOGLOBINEMIA; RISK FACTORS; VICIA FABA;

EID: 67349287562     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-009-0952-x     Document Type: Review

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