Remodeling of dystrophin and sarcomeric Z-band occurs in pediatric cardiomyopathies: A unifying mechanism for force transmission defect

Journal of Cardiovascular Medicine

Volumn 10, Issue 2, 2009, Pages 149-156

  Vatta, Matteo ^a   Sinagra, Gianfranco ^b   Brunelli, Luca ^c   Faulkner, Georgine ^d  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF TRIESTE   (Italy)

^c UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

^d INTERNATIONAL CENTRE FOR GENETIC ENGINEERING AND BIOTECHNOLOGY   (Italy)

Author keywords

Cardiomyopathy; Congestive heart failure; Dystrophin; Dystrophin associated glycoprotein complex; Sarcomere

Indexed keywords

DELTA SARCOGLYCAN; DYSTROPHIN; FATTY ACID BINDING PROTEIN; GLYCOPROTEIN; DMD PROTEIN, HUMAN;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CONGESTIVE CARDIOMYOPATHY; DELETION MUTANT; GENE DELETION; GENE MUTATION; HEART CONTRACTION; HEART MUSCLE; HUMAN; IMMUNOHISTOCHEMISTRY; INFANT; MYOCARDITIS; PEDIATRICS; PRESCHOOL CHILD; RNA SPLICING; SARCOLEMMA; SARCOMERE; SCHOOL CHILD; SYSTOLIC DYSFUNCTION; CHEMISTRY; FEMALE; MALE; METABOLISM; PATHOPHYSIOLOGY;

ADOLESCENT; CARDIOMYOPATHY, DILATED; CHILD; CHILD, PRESCHOOL; DYSTROPHIN; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; INFANT; MALE; MYOCARDIAL CONTRACTION; MYOCARDIUM; SARCOMERES;

EID: 65549160130     PISSN: 15582027     EISSN: None     Source Type: Journal    
DOI: 10.2459/JCM.0b013e328318954c     Document Type: Article

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