Type 2B von willebrand disease associated with the release of platelet agglutinates from megakaryocytes in the bone marrow

Journal of Pediatric Hematology/Oncology

Volumn 30, Issue 9, 2008, Pages 708-711

  Slayton, William B ^a,f   Patel, Milin ^a   Sola Visner, Martha ^b,c   Harris, Neil ^d   Rivers, Angela ^a   Montgomery, Robert R ^e   Friedman, Kenneth D ^e  

^a Department of Pediatrics ^*  (United States)

^b DREXEL UNIVERSITY COLLEGE OF MEDICINE   (United States)

^c ST CHRISTOPHER'S HOSPITAL FOR CHILDREN   (United States)

^d UNIVERSITY OF FLORIDA   (United States)

^e BLOOD RESEARCH INSTITUTE   (United States)

^f UNIVERSITY OF FLORIDA HEALTH   (United States)

Author keywords

Megakaryocyte; Platelet clumps; Pseudothrombocytopenia; Type 2B; Von Willebrand disease

Indexed keywords

VON WILLEBRAND FACTOR;

AMINO ACID SUBSTITUTION; ARTICLE; BLEEDING TENDENCY; BONE MARROW; BONE MARROW BIOPSY; CASE REPORT; CHILD; GENE MUTATION; HUMAN; LABORATORY TEST; MALE; MEGAKARYOCYTE; MEGAKARYOPOIESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; SEQUENCE ANALYSIS; THROMBOCYTE AGGREGATION; THROMBOCYTE RELEASE REACTION; THROMBOCYTOPENIA; TYPE 2B VON WILLEBRAND DISEASE; VON WILLEBRAND DISEASE;

AGGLUTINATION; BLOOD PLATELETS; BONE MARROW EXAMINATION; CHILD; HUMANS; MALE; MEGAKARYOCYTES; MUTATION; THROMBOCYTOPENIA; VON WILLEBRAND DISEASES; VON WILLEBRAND FACTOR;

EID: 65349161369     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0b013e31817541cd     Document Type: Article

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