Clinical improvement of a patient with severe Wilson's disease after a single session of therapeutic plasma exchange

Journal of Clinical Apheresis

Volumn 24, Issue 1, 2009, Pages 25-27

  Hursitoglu, Mehmet ^a   Kara, Osman ^a   Cikrikcioglu, Mehmet A ^a   Celepkulu, Tahsin ^a   Aydin, Sengul ^a   Tukek, Tufan ^a  

^a VAKIF GUREBA TRAINING AND RESEARCH HOSPITAL   (Turkey)

Author keywords

Cirrhosis; Hemolytic anemia; Therapeutic plasma exchange; Wilson's disease

Indexed keywords

PENICILLAMINE; ZINC;

ADOLESCENT; ARTICLE; CASE REPORT; CLINICAL EFFECTIVENESS; COOMBS POSITIVE HEMOLYTIC ANEMIA; DISEASE DURATION; DISEASE SEVERITY; FEMALE; HUMAN; LIVER CIRRHOSIS; PLASMAPHERESIS; TREATMENT DURATION; TREATMENT RESPONSE; WILSON DISEASE;

ADOLESCENT; ANEMIA, HEMOLYTIC; FEMALE; HEPATOLENTICULAR DEGENERATION; HUMANS; LIVER CIRRHOSIS; PLASMA EXCHANGE; TREATMENT OUTCOME;

EID: 63249100303     PISSN: 07332459     EISSN: 10981101     Source Type: Journal    
DOI: 10.1002/jca.20186     Document Type: Article

References (12)

1. Schilsky ML. Wilson disease: genetic basis of copper toxicity and natural history. Semin Liver Dis 1996;16:83-95.
2. Wang XH, Cheng F, Zhang F, Li XC, Qian JM, Kong LB, Zhang H, Li GQ. Copper metabolism after living related liver transplantation for Wilson's disease. World J Gastroenterol 2003;9:2836-2838.
3. Stracciari A, Tempestini A, Borghi A, Guarino M. Effect of liver transplantation on neurological manifestations in Wilson disease. Arch Neurol 2000;57:384-386.
4. Kinebuchi M, Matsuura A, Ohya K, Abo W, Kitazawa J. Contribution of Va24Vb11 natural killer T cells in Wilsonian hepatitis. Clin Exp Immunol 2005;139:144-151.
5. Lee JJ, Kim HJ, Chung IJ, Kook H, Byun JR, Kwon SY, Park MR, Choi KS, Hwang TJ, Ryang DW. Acute hemolytic crisis with fulminant hepatic failure as the first manifestation of Wilson's disease: a case report. J Korean Med Sci 1998;13:548-550.
6. Nagata Y, Uto H, Hasuike S, Ido A, Hayashi K, Eto T, Hamakawa T, Tanaka K, Tsubouchi H. Bridging use of plasma exchange and continuous hemodiafiltration before living donor liver transplantation in fulminant Wilson's disease. Intern Med 2003;42:967-970.
7. Asfaha S, Almansori M, Qarni U, Gutfreund KS. Plasmapheresis for hemolytic crisis and impending acute liver failure in Wilson disease. J Clin Apher 2007;22:295-298.
8. Mokhlesi B, Leiken JB, Murray P, Corbridge TC. Adult toxicology in critical care. I. General approach to the intoxicated patient. Chest 2003;123:577-592.
9. Winchester JF. Dialysis and hemoperfusion in poisoning. Adv Ren Replace Ther 2002;9:26-30.
10. Takeda T, Yukioka T, Shimazaki S. Cupric sulfate intoxication with rhabdomyolysis, treated with chelating agents and blood purification. Intern Med 2000;39:253-255.
11. Jhang JS, Schilsky ML, Lefkowitch JH, Schwartz J. Therapeutic plasmapheresis as a bridge to liver transplantation in fulminant Wilson disease. J Clin Apher 2007;22:10-14.
12. Dabrowska E, Jabłońska-Kaszewska I, Oziebłowski A, Falkiewicz B. Acute haemolytic syndrome and liver failure as the first manifestations of Wilson's disease. Med Sci Monit 2001;7 (Suppl 1):246-251.