Hemophilia severity score system: Validation from an Italian Regional Hemophilia Reference Center

Journal of Thrombosis and Haemostasis

Volumn 7, Issue 4, 2009, Pages 720-722

  Tagliaferri, Annarita ^a   Di Perna, C ^a   Franchini, M ^a   Rivolta, G F ^a   Pattacini, C ^a  

^a UNIVERSITY HOSPITAL OF PARMA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

BLOOD CLOTTING FACTOR 5 LEIDEN; PROTHROMBIN;

ADULT; CHILD; DISEASE SEVERITY; GENETIC POLYMORPHISM; HEMOPHILIA A; HEMOPHILIA B; HUMAN; ITALY; LETTER; MAJOR CLINICAL STUDY; PHENOTYPE; PRIORITY JOURNAL; SCHOOL CHILD; SCORING SYSTEM; THROMBOSIS PREVENTION; VALIDATION PROCESS;

ADULT; HEMOPHILIA A; HUMANS; ITALY; PREMEDICATION; REGISTRIES; SEVERITY OF ILLNESS INDEX; THROMBOPHILIA; YOUNG ADULT;

EID: 63049121902     PISSN: 15387933     EISSN: 15387836     Source Type: Journal    
DOI: 10.1111/j.1538-7836.2009.03288.x     Document Type: Letter

References (9)

1. Schulman S, Eelde A, Holmström M, Ståhlberg G, Odeberg J, Blombäck M. Validation of a composite score for clinical severity of hemophilia. J Thromb Haemost 2008; 6: 1113-21.
2. Tagliaferri A, Marietta M, Calizzani G, Busetti S. Hub and spoke: organization model for haemophilia centres of Emilia-Romagna Region. Haemophilia 2002; 8: Abstr PO42.
3. Tagliaferri A, Rivolta GF, Biasoli C, Valdrè L, Rodorigo G, D'Incà M, Moratelli S, Albertini P, Vincenzi D, Arbasi MC, Marietta M, Pattacini C. A web-based registry of inherited bleeding disorders in the region of Emilia-Romagna: Results at three and half years. Haemophilia 2008; 14: 343-54.
4. Pattacini C, Rivolta GF, Di Perna C, Riccardi F, Tagliaferri A. A web based clinical record 'xl'Emofilia®'for outpatients with haemophilia and allied disorders in the Region of Emilia-Romagna: Features and pilot use. Haemophilia 2008; 15: 150-8.
5. Tagliaferri A, Franchini M, Coppola A, Rivolta GF, Santoro C, Rossetti G, Zanon E, Dragani A, Iannaccaro P, Radossi P, Mannucci PM. Effects of secondary prophylaxis started in adolescent and adult haemophiliacs. Haemophilia 2008; 14: 945-51.
6. Manco-Johnson MJ, Abshire TC, Shapiro AD, Riske B, Hacker MR, Kilcoyne R, Ingram JD, Manco-Johnson ML, Funk S, Jacobson L, Valentino LA, Hoots WK, Buchanan GR, DiMichele D, Recht M, Brown D, Leissinger C, Bleak S, Cohen A, Mathew P, et al. Prophylaxis versus episodic treatment to prevent joint disease in boys with severe hemophilia. New Engl J Med 2007; 357: 535-44.
7. Nilsson IM, Berntorp E, Löfqvist T, Pettersson H. Twenty-five years' experience of prophylactic treatment in severe haemophilia A and B. J Intern Med 1992; 232: 25-32.
8. Astermak J, Petrini P, Tengborn L, Schulman S, Ljung R, Bertorp E. Primary prophylaxis in severe haemophilia should be started at an early age but can be individualized. Br J Haematol 1999; 105: 1109-13.
9. Franchini M, Mannucci PM. Interactions between genotype and phenotype and thrombosis. Haematologica 2008; 93: 649-52.