Amino acids levels and lipid peroxidation in maple syrup urine disease patients

Clinical Biochemistry

Volumn 42, Issue 6, 2009, Pages 462-466

  Barschak, Alethéa G ^a,b   Sitta, Angela ^a,b   Deon, Marion ^a,b   Busanello, Estela N B ^b   Coelho, Daniella M ^b   Cipriani, Franciele ^a   Dutra Filho, Carlos S ^a   Giugliani, Roberto ^b   Wajner, Moacir ^a,b   Vargas, Carmen R ^a,b  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

Antioxidant defenses; Lipid peroxidation; Maple syrup urine disease; Methionine; Oxidative stress; Tryptophan

Indexed keywords

2 HYDROXYACID; 2 OXOACID; 2 OXOISOCAPROIC ACID; 2 OXOISOVALERIC ACID; ALANINE; ALLOISOLEUCINE; AMINO ACID; ANTIOXIDANT; ASPARTIC ACID; BRANCHED CHAIN AMINO ACID; GLUTAMIC ACID; GLUTAMINE; GLYCINE; HISTIDINE; HYDROXYACID; ISOLEUCINE; LEUCINE; LIPID; LYSINE; METHIONINE; ORNITHINE; OXOACID; PHENYLALANINE; SERINE; THIOBARBITURIC ACID; THIOBARBITURIC ACID REACTIVE SUBSTANCE; TRYPTOPHAN; TYROSINE; UNINDEXED DRUG; VALINE;

ADULT; AMINO ACID BLOOD LEVEL; ANTIOXIDANT ACTIVITY; ARTICLE; BIOACCUMULATION; BLOOD SAMPLING; CLINICAL ARTICLE; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; HUMAN; LIPID PEROXIDATION; MAPLE SYRUP URINE DISEASE; MEASUREMENT; METABOLITE; OXIDATIVE STRESS; PRIORITY JOURNAL;

ADULT; AMINO ACIDS; ANTIOXIDANTS; HUMANS; HYDROXY ACIDS; ISOLEUCINE; KETO ACIDS; LEUCINE; LIPID PEROXIDATION; MAPLE SYRUP URINE DISEASE; METHIONINE; OXIDATIVE STRESS; THIOBARBITURIC ACID REACTIVE SUBSTANCES; TRYPTOPHAN; VALINE;

EID: 61849160434     PISSN: 00099120     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.clinbiochem.2008.12.005     Document Type: Article

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