Fatal rupture of pulmonary arteriovenous malformation in hereditary haemorrhagic telangiectasis and severe PAH

European Respiratory Review

Volumn 18, Issue 111, 2009, Pages 42-46

  Montani, D ^a,d   Price, L C ^a   Girerd, B ^a   Chinet, T ^b   Lacombe, P ^c   Simonneau, G ^a   Humbert, M ^a  

^a UNIVERSITÉ PARIS SACLAY   (France)

^b Service de Pneumologie   (France)

^c ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

^d HÔPITAL ANTOINE BÉCLÈRE   (France)

Author keywords

Activin receptor like kinase 1; Arteriovenous malformation; Embolisation; Hereditary haemorrhagic telangiectasia; Pulmonary arterial hypertension; Rupture

Indexed keywords

ACTIVIN RECEPTOR LIKE KINASE 1; ENDOTHELIN RECEPTOR ANTAGONIST; ILOPROST;

ADULT; ARTICLE; ARTIFICIAL EMBOLISM; CASE REPORT; DISEASE ASSOCIATION; DISEASE SEVERITY; DOPPLER ECHOCARDIOGRAPHY; FEMALE; GENETIC ANALYSIS; HEART CATHETERIZATION; HEMODYNAMICS; HUMAN; MISSENSE MUTATION; PULMONARY ARTERIOVENOUS FISTULA; PULMONARY HYPERTENSION; RADIODENSITOMETRY; RENDU OSLER WEBER DISEASE; RISK ASSESSMENT; RUPTURE; THORAX RADIOGRAPHY; TREATMENT CONTRAINDICATION;

ADULT; ARTERIOVENOUS MALFORMATIONS; EMBOLIZATION, THERAPEUTIC; FATAL OUTCOME; FEMALE; HUMANS; HYPERTENSION, PULMONARY; PULMONARY ARTERY; PULMONARY VEINS; RUPTURE, SPONTANEOUS; TELANGIECTASIA, HEREDITARY HEMORRHAGIC;

EID: 61649114738     PISSN: 09059180     EISSN: None     Source Type: Journal    
DOI: 10.1183/09059180.00011113     Document Type: Article

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