Cerebral edema and intracranial hypertension in an adult with maple syrup urine disease

European Journal of Neurology

Volumn 16, Issue 3, 2009, Pages

  Sutter, R ^a   Killer, H E ^b   Bilz, S ^a   Baumgartner, M ^c   Ott, H W ^a   Steck, A J ^a   Renaud, S ^a  

^a UNIVERSITY HOSPITAL BASEL   (Switzerland)

^b CANTONAL HOSPITAL AARAU   (Switzerland)

^c UNIVERSITY HOSPITAL ZURICH   (Switzerland)

Author keywords

Amino acids; Inherited metabolic disorders; Metabolic and endocrine disorders; Neuro ophthalmology

Indexed keywords

ACETAZOLAMIDE; CARBOHYDRATE; ISOLEUCINE; LEUCINE; VALINE;

ADULT; BRAIN EDEMA; CASE REPORT; COGNITION; DIET SUPPLEMENTATION; DISEASE COURSE; FENESTRATION; HUMAN; INTRACRANIAL HYPERTENSION; LETTER; LUMBAR PUNCTURE; MALE; MAPLE SYRUP URINE DISEASE; METABOLIC REGULATION; NERVE SHEATH; NEUROLOGIC EXAMINATION; NUCLEAR MAGNETIC RESONANCE IMAGING; OPTIC NERVE; PAPILLEDEMA; PRIORITY JOURNAL; PROTEIN DEGRADATION; RETINA HEMORRHAGE;

AGE OF ONSET; BRAIN; BRAIN EDEMA; DIAGNOSIS, DIFFERENTIAL; HUMANS; INTRACRANIAL HYPERTENSION; MAGNETIC RESONANCE IMAGING; MALE; MAPLE SYRUP URINE DISEASE; PAPILLEDEMA; YOUNG ADULT;

EID: 60049097225     PISSN: 13515101     EISSN: 14681331     Source Type: Journal    
DOI: 10.1111/j.1468-1331.2008.02425.x     Document Type: Letter

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