Evaluation of endogenous nitric oxide synthesis in congenital urea cycle enzyme defects

Metabolism: Clinical and Experimental

Volumn 58, Issue 3, 2009, Pages 278-282

  Nagasaka, Hironori ^a   Tsukahara, Hirokazu ^b   Yorifuji, Tohru ^c   Miida, Takashi ^d   Murayama, Kei ^a   Tsuruoka, Tomoko ^a   Takatani, Tomozumi ^a   Kanazawa, Masaki ^e   Kobayashi, Kunihiko ^f   Okano, Yoshiyuki ^g   Takayanagi, Masaki ^a  

^a CHIBA CHILDREN'S HOSPITAL   (Japan)

^b UNIVERSITY OF FUKUI HOSPITAL   (Japan)

^c KYOTO UNIVERSITY HOSPITAL   (Japan)

^d JUNTENDO UNIVERSITY   (Japan)

^e Chiba Children's Hospital   (Japan)

^f HOKKAIDO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^g OSAKA CITY UNIVERSITY HOSPITAL   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; ARGININOSUCCINATE LYASE; ARGININOSUCCINATE SYNTHASE; CITRULLINE; N(G),N(G) DIMETHYLARGININE; NITRATE; NITRIC OXIDE SYNTHASE; NITRIC OXIDE SYNTHASE INHIBITOR; NITRITE; ORNITHINE CARBAMOYLTRANSFERASE;

ADULT; ARTICLE; CHILD; CITRULLINEMIA; CLINICAL ARTICLE; CLINICAL EVALUATION; CLINICAL FEATURE; CONTROL GROUP; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; ENZYME ACTIVITY; ENZYME DEFECT; FEMALE; HUMAN; MALE; MEASUREMENT; PATHOPHYSIOLOGY; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SYNTHESIS; SCHOOL CHILD; STATISTICAL SIGNIFICANCE; UREA CYCLE; UREA CYCLE ENZYME DEFECT;

ARGININE; ARGININOSUCCINATE LYASE; ARGININOSUCCINATE SYNTHASE; CHILD, PRESCHOOL; CITRULLINE; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; MALE; NITRIC OXIDE; NITRIC OXIDE SYNTHASE; ORNITHINE CARBAMOYLTRANSFERASE; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; UREA;

EID: 59649120881     PISSN: 00260495     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.metabol.2008.09.025     Document Type: Article

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