Cystic fibrosis: Evolution from a fatal disease of infancy with a clear phenotype to a chronic disease of adulthood with diverse manifestations

Clinical Reviews in Allergy and Immunology

Volumn 35, Issue 3, 2008, Pages 97-99

  Ren, Clement L ^a  

^a UNIVERSITY OF ROCHESTER   (United States)

Author keywords

Bacterial infections; Bronchiectasis; Gene therapy; Genetic disorders; Inflammation

Indexed keywords

TRANSMEMBRANE CONDUCTANCE REGULATOR; CFTR PROTEIN, HUMAN; UNCLASSIFIED DRUG;

BRONCHITIS; CAUCASIAN; CHRONIC DISEASE; CLINICAL FEATURE; CYSTIC FIBROSIS; DISEASE COURSE; DISEASE EXACERBATION; FATALITY; GENE MUTATION; GENETIC ASSOCIATION; HUMAN; INFANCY; PATHOPHYSIOLOGY; PHENOTYPE; PSEUDOMONAS AERUGINOSA; SHORT SURVEY; ADULT; EDITORIAL; GENETICS; MUTATION; NEWBORN;

ADULT; CHRONIC DISEASE; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DISEASE PROGRESSION; EUROPEAN CONTINENTAL ANCESTRY GROUP; HUMANS; INFANT, NEWBORN; MUTATION;

EID: 59449101370     PISSN: 10800549     EISSN: None     Source Type: Journal    
DOI: 10.1007/s12016-008-8077-y     Document Type: Short Survey

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