Does satellite cell dysfunction contribute to disease progression in Emery-Dreifuss muscular dystrophy?

Biochemical Society Transactions

Volumn 36, Issue 6, 2008, Pages 1344-1349

  Gnocchi, Viola F ^a   Ellis, Juliet A ^a   Zammit, Peter S ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

Emerin; Emery Dreifuss muscular dystrophy (EDMD); Lamin; MyoD; Nuclear envelope; Retinoblastoma protein; Satellite cell

Indexed keywords

EMERIN; LAMIN A; LAMIN;

CELL NUCLEUS MEMBRANE; CELL REGENERATION; CONFERENCE PAPER; DISEASE COURSE; DUCHENNE MUSCULAR DYSTROPHY; EMERY DREIFUSS MUSCULAR DYSTROPHY; GENE EXPRESSION; GENE MUTATION; HUMAN; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE INJURY; MUSCLE REGENERATION; MUSCLE WEAKNESS; MYOBLAST; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SATELLITE CELL; SKELETAL MUSCLE; STEM CELL; ANIMAL; DISEASE MODEL; GENETICS; METABOLISM; MUSCLE DEVELOPMENT; PATHOLOGY; PATHOPHYSIOLOGY; REVIEW; SKELETAL MUSCLE SATELLITE CELL;

ANIMALS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; HUMANS; LAMINS; MUSCLE DEVELOPMENT; MUSCULAR DYSTROPHY, EMERY-DREIFUSS; SATELLITE CELLS, SKELETAL MUSCLE;

EID: 59149094933     PISSN: 03005127     EISSN: 14708752     Source Type: Journal    
DOI: 10.1042/BST0361344     Document Type: Conference Paper

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