Fever of unclear origin and cytopenia because of acute splenic sequestration in a young immunocompetent carrier of beta-globin mutation for Hb valletta

American Journal of the Medical Sciences

Volumn 336, Issue 6, 2008, Pages 508-511

  Parrinello, Gaspare ^a   Torres, Daniele ^a,b   Paterna, Salvatore ^a   Di Pasquale, Pietro ^a   Licata, Giuseppe ^a  

^a UNIVERSITY OF PALERMO   (Italy)

^b NONE   (Italy)

Author keywords

Acute splenic sequestration crises; Beta thalassemia; Fever of unclear origin; Hb Valletta; Leucothrombocytopenia; Splenomegaly; Still?s skin rash

Indexed keywords

HEMOGLOBIN; HEMOGLOBIN VALETTA; SULTAMICILLIN; UNCLASSIFIED DRUG; BETA GLOBIN; HEMOGLOBIN VALLETTA; HEMOGLOBIN VARIANT;

ADOLESCENT; AMINO ACID SUBSTITUTION; ANEMIA; ARTICLE; BETA GLOBIN GENE; BONE MARROW BIOPSY; BONE MARROW DISEASE; BONE MARROW HYPERPLASIA; CASE REPORT; CYTOPENIA; DISEASE EXACERBATION; FATIGUE; FOLLOW UP; GENE; GENE MUTATION; GENETIC ANALYSIS; GENETIC POLYMORPHISM; HEALTH; HEMOGLOBINOPATHY; HEPATOMEGALY; HEPATOSPLENOMEGALY; HETEROZYGOSITY; HOMOZYGOSITY; HOSPITAL ADMISSION; HUMAN; IMMUNOCOMPETENCE; INFECTION; IRON DEFICIENCY ANEMIA; LEUKOPENIA; MALE; MICROCYTOSIS; MYALGIA; NUCLEOTIDE SEQUENCE; PRURITUS; PYREXIA IDIOPATHICA; RASH; RECURRENT FEVER; REMISSION; SPLEEN DISEASE; SPLEEN SEQUESTRATION; SPLENOMEGALY; THALASSEMIA; THROMBOCYTOPENIA; UNIVERSITY HOSPITAL; ADULT; BLOOD; CHILD; FEVER; GENETICS; HEMATOLOGIC DISEASE; MUTATION; PATHOLOGY; PATHOPHYSIOLOGY; SPLEEN;

ADOLESCENT; ADULT; ANEMIA; BETA-GLOBINS; CHILD; FEVER; HEMATOLOGIC DISEASES; HEMOGLOBINS, ABNORMAL; HUMANS; IMMUNOCOMPETENCE; MALE; MUTATION; SPLEEN;

EID: 59049095964     PISSN: 00029629     EISSN: None     Source Type: Journal    
DOI: 10.1097/MAJ.0b013e318162d13f     Document Type: Article

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