Proportion between wild-type and mutant protein in truncated compared to full-length ATTR: An analysis on transplanted transthyretin T60A amyloidosis patients

Biochemical and Biophysical Research Communications

Volumn 379, Issue 4, 2009, Pages 846-850

  Ihse, Elisabet ^a   Stangou, Arie J ^b   Heaton, Nigel D ^b   O'Grady, John ^b   Ybo, Anna ^a   Hellman, Ulf ^c   Edvinsson, Åsa ^a   Westermark, Per ^a  

^a UPPSALA UNIVERSITY   (Sweden)

^b KING S COLLEGE HOSPITAL   (United Kingdom)

^c Ludwig Instimte for Cancer Research   (Sweden)

Author keywords

Amyloid; ATTRT60A; Cardiomyopathy; Familial amyloidotic polyneuropathy; Fibril; Liver transplantation; Transthyretin; Wild type

Indexed keywords

MUTANT PROTEIN; PLASMA PROTEIN; PREALBUMIN;

ADULT; AGED; AMYLOIDOSIS; ANAMNESIS; ARTICLE; CANCER PATIENT; CANCER SURVIVOR; CARDIOMYOPATHY; CASE REPORT; CLINICAL FEATURE; FAMILIAL AMYLOID POLYNEUROPATHY; FIBER; GRAFT RECIPIENT; HUMAN; LIVER GRAFT; MALE; MASS SPECTROMETRY; MORTALITY; OUTCOME ASSESSMENT; PATHOGENESIS; PATIENT INFORMATION; POINT MUTATION; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BLOOD LEVEL; SURVIVAL TIME; TREATMENT OUTCOME;

AGED; AMINO ACID SEQUENCE; AMYLOIDOSIS, FAMILIAL; HUMANS; LIVER TRANSPLANTATION; MALE; MIDDLE AGED; MOLECULAR SEQUENCE DATA; MYOCARDIUM; PEPTIDE FRAGMENTS; PREALBUMIN;

EID: 58949100102     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2008.12.095     Document Type: Article

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