A Griscelli syndrome type 2 murine model of hemophagocytic lymphohistiocytosis (HLH)

European Journal of Immunology

Volumn 38, Issue 11, 2008, Pages 3219-3225

  Schmid, Jana Pachlopnik ^a,b,c   Ho, Chen Hsuan ^a,b   Diana, Julien ^d   Pivert, Gérard ^c   Lehuen, Agnès ^d   Geissmann, Frédéric ^b,c   Fischer, Alain ^a,b,c   de Saint Basile, Geneviève ^a,b,c  

^a INSERM   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

^d HÔPITAL SAINT VINCENT DE PAUL   (France)

Author keywords

Animal models; Clinical immunology; Cytotoxicity; Immunodeficiencies

Indexed keywords

AMINOTRANSFERASE; GAMMA INTERFERON; RAB27A PROTEIN; TRIACYLGLYCEROL; RAB PROTEIN; RAB27A PROTEIN, MOUSE; UNCLASSIFIED DRUG;

AMINOTRANSFERASE BLOOD LEVEL; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BODY WEIGHT; CONTROLLED STUDY; DISEASE MARKER; ERYTHROPHAGOCYTOSIS; FEVER; GRISCELLI SYNDROME; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HEPATOMEGALY; HISTOPATHOLOGY; HYPERTRIGLYCERIDEMIA; IMMUNE RESPONSE; LYMPHADENOPATHY; LYMPHOCYTIC CHORIOMENINGITIS VIRUS; LYMPHOCYTIC INFILTRATION; MOUSE; NONHUMAN; PANCYTOPENIA; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; SPLENOMEGALY; TRIACYLGLYCEROL BLOOD LEVEL; VIRUS INDUCTION; WASTING SYNDROME; WEIGHT REDUCTION; ANIMAL; C3H MOUSE; C57BL MOUSE; DISEASE MODEL; GENETICS; MUTATION; PATHOLOGY; SYNDROME; VIRUS MENINGITIS;

ANIMALS; DISEASE MODELS, ANIMAL; LYMPHOCYTIC CHORIOMENINGITIS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MICE; MICE, INBRED C3H; MICE, INBRED C57BL; MUTATION; RAB GTP-BINDING PROTEINS; SYNDROME;

EID: 58149354327     PISSN: 00142980     EISSN: 15214141     Source Type: Journal    
DOI: 10.1002/eji.200838488     Document Type: Article

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