Recombinant collagen studies link the severe conformational changes induced by osteogenesis imperfecta mutations to the disruption of a set of interchain salt bridges

Journal of Biological Chemistry

Volumn 283, Issue 49, 2008, Pages 34337-34344

  Xu, Ke ^a   Nowak, Iwona ^a   Kirchner, Michele ^a   Xu, Yujia ^a  

^a CITY UNIVERSITY OF NEW YORK   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ESCHERICHIA COLI; MOLECULAR INTERACTIONS; PORT TERMINALS;

BIOPHYSICAL CHARACTERIZATIONS; BONE DISEASES; COLLAGEN TRIPLE HELIXES; CONFORMATIONAL CHANGES; HELICAL CONFORMATIONS; LOCAL INTERACTIONS; LONG RANGES; MUTATION SITES; NEW MECHANISMS; OSTEOGENESIS; OSTEOGENESIS IMPERFECTA; PROTEASE DIGESTIONS; SALT BRIDGES; SUBSTITUTION MUTATIONS; TERMINAL REGIONS; TRIPLE HELIXES; UNSTABLE REGIONS;

COLLAGEN;

COLLAGEN; COLLAGEN TYPE 1; GLYCINE; PROTEINASE; RECOMBINANT COLLAGEN; SERINE; TYPE 1 COLLAGEN ALPHA1; UNCLASSIFIED DRUG;

AMINO ACID SUBSTITUTION; ARTICLE; CARBOXY TERMINAL SEQUENCE; CONFORMATIONAL TRANSITION; DISEASE SEVERITY; GENE DISRUPTION; GENE MUTATION; MOLECULAR MODEL; MOLECULAR STABILITY; OSTEOGENESIS IMPERFECTA; PRIORITY JOURNAL; SITE DIRECTED MUTAGENESIS;

AMINO ACID SEQUENCE; CHYMOTRYPSIN; CIRCULAR DICHROISM; COLLAGEN; ESCHERICHIA COLI; HUMANS; MOLECULAR SEQUENCE DATA; MUTATION; OSTEOGENESIS IMPERFECTA; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN STRUCTURE, SECONDARY; RECOMBINANT PROTEINS; SALTS; SPECTROMETRY, MASS, MATRIX-ASSISTED LASER DESORPTION-IONIZATION;

ESCHERICHIA COLI;

EID: 57749112119     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M805485200     Document Type: Article

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