Three-dimensional CT and histopathological findings of airway malacia in Hunter syndrome

Tokai Journal of Experimental and Clinical Medicine

Volumn 32, Issue 2, 2007, Pages 59-61

  Nagano, Reiko ^a   Takizawa, Shunya ^a   Hayama, Naoki ^a   Umemura, Shinobu ^a   Uesugi, Tsuyoshi ^a   Nakagawa, Satoko ^a   Okamoto, Sari ^a   Yanagimachi, Noriharu ^a   Takagi, Shigeharu ^a  

^a TOKAI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Airway malacia; Bronchial 3DCT; Bronchoscopy; Hunter syndrome

Indexed keywords

GLYCOSAMINOGLYCAN; OXYGEN;

ADULT; ARTICLE; AUTOPSY; BRONCHOMALACIA; BRONCHOSCOPY; BRONCHUS STENOSIS; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; CORRELATION ANALYSIS; DEATH; DISEASE SEVERITY; DYSPNEA; GRANULATION TISSUE; HISTOPATHOLOGY; HOME OXYGEN THERAPY; HOSPITAL ADMISSION; HUMAN; HUNTER SYNDROME; MALE; MEDICAL DECISION MAKING; RESPIRATORY DISTRESS; RISK ASSESSMENT; THREE DIMENSIONAL IMAGING; TRACHEA STENOSIS; TRACHEOMALACIA; TRACHEOSTOMY;

FATAL OUTCOME; HUMANS; IMAGING, THREE-DIMENSIONAL; MALE; MUCOPOLYSACCHARIDOSIS II; TOMOGRAPHY, X-RAY COMPUTED; TRACHEAL STENOSIS; YOUNG ADULT;

EID: 57149093240     PISSN: 03850005     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (5)

1. Neufeld EF, Muenzer J. The mucopolysarcharidoses. In: The Metabolic and Molecular Bases of Inherited Disease, Scriver. CR Beaudet AL Sly WS Valle D eds. 8th cd. McGraw-Hill, New York, 2001: 3421-3452.
2. Morehead JM, Parsons DS. Tracheobrouchomalacia in Hunter's syndrome. Int J Pediatr Otorhinolaryngol 26: 255-261, 1993.
3. Semenza GL, Pyeritz RE. Respiratory complications of mucopolysaccharide storage disorders. Medicine (Baltimore) 67: 209-219, 1988.
4. Davitt SM, Hatrick A, Sabharwal T, Pearce A, Gleeson M, Adam A. Tracheobronchial stent insertions in the management of major airway obstruction in a patient with Hunter midrome (type-II mucopolysacdiaridosis). Eur R adiol. 12: 458-462, 2002.
5. Sonnet JR, Keenan RJ, Ferson PF, Griffith BP, Landreneau RJ. Exidobronchial management of benign, malignant and lung transplantation airway stenoses. Ann Thorac Surg 59: 1417-1422, 1995.