Overexpressed mitochondrial leucyl-tRNA synthetase suppresses the A3243G mutation in the mitochondrial tRNALeu(UUR) gene

RNA

Volumn 14, Issue 11, 2008, Pages 2407-2416

  Park, Hyejeong ^a   Davidson, Edgar ^a   King, Michael P ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

Author keywords

A3243G mutation; Mitochondria; mtDNA; Suppression; tRNA; tRNA synthetase

Indexed keywords

LEUCINE TRANSFER RNA LIGASE; MITOCHONDRIAL DNA; OXYGEN; TRANSFER RNA;

ANTICODON; ARTICLE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVATION; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE; OXYGEN CONSUMPTION; PRIORITY JOURNAL; PROTEIN FOLDING; RESPIRATORY CHAIN; STEADY STATE;

CELL LINE; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; HUMANS; LEUCINE-TRNA LIGASE; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MUTATION; PROTEIN BIOSYNTHESIS; RNA, TRANSFER, AMINO ACYL; SUPPRESSION, GENETIC;

EID: 55549087221     PISSN: 13558382     EISSN: 14699001     Source Type: Journal    
DOI: 10.1261/rna.1208808     Document Type: Article

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