Steroid-refractory severe hepatic failure in adult onset Still's disease responding to cyclosporine

Clinical Rheumatology

Volumn 27, Issue 11, 2008, Pages 1451-1453

  Nagashima, Takao ^a   Aoki, Yoko ^a   Onishi, Sachiko ^a   Iwamoto, Masahiro ^a   Okazaki, Hitoaki ^a   Minota, Seiji ^a  

^a JICHI MEDICAL UNIVERSITY   (Japan)

Author keywords

Adult onset Still's disease; Cyclosporine; Interleukin 18; Liver failure; Macrophage activation syndrome

Indexed keywords

BETAMETHASONE; CYCLOSPORIN; DEXAMETHASONE; HEPARIN; INDOMETACIN; MELOXICAM; METHOTREXATE; METHYLPREDNISOLONE; PREDNISOLONE; STEROID;

ADULT; ADULT ONSET STILL DISEASE; ARTHRALGIA; ARTICLE; CASE REPORT; CONTINUOUS INFUSION; DISEASE EXACERBATION; DRUG DOSE INCREASE; DRUG INDUCED HEADACHE; DRUG MEGADOSE; DRUG PULSE THERAPY; DRUG RESPONSE; DRUG TREATMENT FAILURE; DRUG WITHDRAWAL; ECHOGRAPHY; FATIGUE; FEMALE; FEVER; HEART PALPITATION; HOSPITAL ADMISSION; HOSPITAL DISCHARGE; HUMAN; HUMAN TISSUE; JAPANESE; LIVER BIOPSY; LIVER FAILURE; LIVER NECROSIS; LIVER TOXICITY; MAINTENANCE THERAPY; PRIORITY JOURNAL; RASH; RELAPSE; REMISSION; SIDE EFFECT; SORE THROAT; THERAPY RESISTANCE;

ADULT; CYCLOSPORINE; ENZYME INHIBITORS; FEMALE; HUMANS; LIVER FAILURE, ACUTE; MIDDLE AGED; STEROIDS; STILL'S DISEASE, ADULT-ONSET; TREATMENT FAILURE;

EID: 53849112274     PISSN: 07703198     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10067-008-0950-9     Document Type: Article

References (15)

1. Pouchot J, Sampalis JS, Beaudet F et al (1991) Adult Still's disease: manifestations, disease course, and outcome in 62 patients. Medicine (Baltimore) 70:118-136
2. McFarlane M, Harth M, Wall WJ (1997) Liver transplant in adult Still's disease. J Rheumatol 24:2038-2041
3. Dino O, Provenzano G, Giannuoli G et al (1996) Fulminant hepatic failure in adult onset Still's disease. J Rheumatol 23:784-785
4. Ogata A, Kitano M, Yamanaka J et al (2003) Interleukin-18 and hepatocyte growth factor in fulminant hepatic failure of adult onset Still's disease. J Rheumatol 30:1093-1096
5. Yamanaka J, Saito S, Kuroda N et al (2003) Successful living related liver transplantation for adult Still's disease. J Gastroenterol Hepatol 18:1109-1110
6. Omagari K, Matsunaga Y, Yamashita H et al (2003) Successful treatment with cyclosporin in adult-onset Still's disease manifesting as acute hepatitis with marked hyperferritinemia. Am J Med Sci 326:148-151
7. Kelly A, Ramanan AV (2007) Recognition and management of macrophage activation syndrome in juvenile arthritis. Curr Opin Rheumatol 19:477-481
8. Schwarz-Eywill M, Heilig B, Bauer H et al (1992) Evaluation of serum ferritin as a marker for adult Still's disease activity. Ann Rheum Dis 51:683-685
9. Kawashima M, Yamamura M, Taniai M et al (2001) Levels of interleukin-18 and its binding inhibitors in the blood circulation of patients with adult-onset Still's disease. Arthritis Rheum 44:550-560
10. Billiau AD, Roskams T, Van Damme-Lombaerts R et al (2005) Macrophage activation syndrome: Characteristic findings on liver biopsy illustrating the key role of activated, IFN-gamma-producing lymphocytes and IL-6- and TNF-alpha-producing macrophages. Blood 105:1648-1651
11. Hoshino T, Ohta A, Yang D et al (1998) Elevated serum interleukin 6, interferon-gamma, and tumor necrosis factor-alpha levels in patients with adult Still's disease. J Rheumatol 25:396-398
12. Marchesoni A, Ceravolo GP, Battafarano N et al (1997) Cyclosporin A in the treatment of adult onset Still's disease. J Rheumatol 24:1582-1587
13. Shojania K, Chalmers A, Rangno K (1995) Cyclosporin A in the treatment of adult Still's disease. J Rheumatol 22:1391-1392
14. Park JH, Bae JH, Choi YS et al (2004) Adult-onset Still's disease with disseminated intravascular coagulation and multiple organ dysfunctions dramatically treated with cyclosporine A. J Korean Med Sci 19:137-141
15. Nishida T, Suzuki K, Kuwada N et al (2001) Hemophagocytic syndrome and adult Still's disease associated with meningoencephalitis and unconsciousness. Intern Med 40:1037-1040