Angiography-negative primary central nervous system vasculitis: A syndrome involving small cerebral vessels

Medicine

Volumn 87, Issue 5, 2008, Pages 264-271

  Salvarani, Carlo ^a,c   Brown, Robert D ^a   Calamia, Kenneth T ^b   Christianson, Teresa J H ^a   Huston, John ^a   Meschia, James F ^b   Giannini, Caterina ^a   Miller, Dylan V ^a   Hunder, Gene G ^a  

^a MAYO CLINIC   (United States)

^b MAYO CLINIC   (United States)

^c S MARIA NUOVA HOSPITAL   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

AZATHIOPRINE; BRAIN PROTEIN; CYCLOPHOSPHAMIDE; DEXAMETHASONE; METHYLPREDNISOLONE; PREDNISONE;

ADULT; AGED; ANOREXIA; APHASIA; ARTICLE; ATAXIA; BRAIN BIOPSY; BRAIN BLOOD VESSEL; BRAIN HEMORRHAGE; BRAIN VASCULITIS; CEREBROSPINAL FLUID; CLINICAL ARTICLE; COGNITIVE DEFECT; COMPARATIVE STUDY; CONFUSION; CONTROLLED STUDY; CONVENTIONAL ANGIOGRAPHY; DEMENTIA; DIPLOPIA; DIZZINESS; DROWSINESS; DRUG DOSE REDUCTION; DRUG PULSE THERAPY; ERYTHROCYTE SEDIMENTATION RATE; FATIGUE; FEMALE; FEVER; HEADACHE; HEMIPARESIS; HUMAN; HUMAN TISSUE; LYMPHOCYTE COUNT; MALE; MENINX; MONOCYTE; NAUSEA; NEUTROPHIL COUNT; NUCLEAR MAGNETIC RESONANCE IMAGING; NYSTAGMUS; PARENCHYMA; PERSONALITY DISORDER; PRIMARY CENTRAL NERVOUS SYSTEM VASCULITIS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; RELAPSE; TRANSIENT ISCHEMIC ATTACK; TREATMENT DURATION; TREATMENT RESPONSE; VERTIGO; VISUAL FIELD DEFECT; VOMITING; WEIGHT REDUCTION; ANGIOGRAPHY; ARTERIOLE; BRAIN ARTERY; BRAIN VEIN; MIDDLE AGED; PATHOLOGY; PROSPECTIVE STUDY; RADIOGRAPHY; SYNDROME; VENULE;

ADULT; AGED; ANGIOGRAPHY; ARTERIOLES; BLOOD SEDIMENTATION; CEREBRAL ARTERIES; CEREBRAL VEINS; FEMALE; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; PROSPECTIVE STUDIES; SYNDROME; VASCULITIS, CENTRAL NERVOUS SYSTEM; VENULES;

EID: 53049103441     PISSN: 00257974     EISSN: None     Source Type: Journal    
DOI: 10.1097/MD.0b013e31818896e1     Document Type: Article

References (19)

1. Benseler SM, deVeber G, Hawkins C, Schneider R, Tyrell PN, Aviv RI, Armstrong D, Laxer RM, Silverman ED. Angiography- negative primary central nervous system vasculitis in children: a newly recognized inflammatory central nervous system disease. Arthritis Rheum. 2005;52:2159-2167.
2. Calabrese LH, Duna GF, Lie JT. Vasculitis in the central nervous system. Arthritis Rheum. 1997;40:1189-1201.
3. Calabrese LH, Gragg LA, Furlan AJ. Benign angiopathy: a distinct subset of angiographically defined primary angiitis of the central nervous system. J Rheumatol. 1993;20:2046-2050.
4. Calabrese LH, Mallek JA. Primary angiitis of the central nervous system: report of 8 new cases, review of the literature, and proposal for diagnostic criteria. Medicine (Baltimore). 1988;67:20-39.
5. Cloft HJ, Phillips CD, Dix JE, McNulty BC, Zagardo MT, Kallmes DF. Correlation of angiography and MR imaging in cerebral vasculitis. Acta Radiol. 1999;40:83-87.
6. Duna GF, George T, Rybicki L, Calabrese LH. Primary angiitis of the central nervous system (PACNS): an analysis of unusual presentations. Arthritis Rheum. 1995;38:S340.
7. Hajj-Ali RA, Furlan A, Abou-Chebel A, Calabrese LH. Benign angiopathy of the central nervous system: cohort of 16 patients with clinical course and long-term follow-up. Arthritis Rheum. 2002; 47:662-669.
8. Harris KG, Tran DD, Sickels WJ, Cornell SH, Yuh WT. Diagnosing intracranial vasculitis: the roles of MR and angiography. AJNR Am J Neuroradiol. 1994;15:317-330.
9. Hassan AS, Trobe JD, McKeever PE, Gebarski SS. Linear magnetic resonance enhancement and optic neuropathy in primary angiitis of the central nervous system. J Neuroophthalmol. 2003;23:127-131.
10. Hurst RW, Grossman RI. Neuroradiology of central nervous system vasculitis. Semin Neurol. 1994;14:320-340.
11. Kadkhodayan Y, Alreshaid A, Moran CJ, Cross DT III, Powers WJ, Derdeyn CP. Primary angiitis of the central nervous system at conventional angiography. Radiology. 2004;233:878-882.
12. MacLaren K, Gillespie J, Shrestha S, Neary D, Ballardie FW. Primary angiitis of the central nervous system: emerging variants. QJM. 2005;98:643-654.
13. Moore PM. Diagnosis and management of isolated angiitis of the central nervous system. Neurology. 1989;39:167-173.
14. Negishi C, Sze G. Vasculitis presenting as primary leptomeningeal enhancement with minimal parenchymal findings. AJNR Am J Neuroradiol. 1993;14:26-28.
15. Parisi JE, Moore PM. The role of biopsy in vasculitis of the central nervous system. Semin Neurol. 1994;14:341-348.
16. Rucker JC, Biousse V, Newman NJ. Leptomeningeal enhancement and venous abnormalities in granulomatous angiitis of the central nervous system. J Neuroophthalmol. 2003;23:148-150.
17. Salvarani C, Brown RD Jr, Calamia K, Christianson TJH, Weigand SD, Miller DV, Giannini C, Meschia JF, Huston J III, Hunder GG. Primary central nervous system vasculitis: analysis of 101 cases. Ann Neurol. 2007;62:442-451.
18. Shoemaker EI, Lin ZS, Rae-Grant AD, Little B. Primary angiitis of the central nervous system: unusual MR appearance. AJNR Am J Neuro-radiol. 1994;15:331-334.
19. Sulter G, Steen C, De Keyser J. Use of the Barthel Index and modified Rankin Scale in acute stroke trials. Stroke. 1999;30:1538-1541.