Paroxysmal nocturnal hemoglobinuria in childhood and adolescence - A retrospective analysis of 18 cases

Indian Journal of Pediatrics

Volumn 75, Issue 6, 2008, Pages 575-578

  Naithani, Rahul ^a   Mahapatra, Manoranjan ^a   Dutta, Pankhi ^a   Kumar, Rajat ^a   Pati, Hara Prasad ^a   Choudhry, Ved Prakash ^a  

^a ALL INDIA INSTITUTE OF MEDICAL SCIENCES   (India)

Author keywords

Aplastic anemia; Children; PNH; Thrombosis

Indexed keywords

ADOLESCENT; APLASTIC ANEMIA; ARTICLE; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; FEMALE; FLOW CYTOMETRY; HUMAN; IMMUNOPHENOTYPING; MALE; PAROXYSMAL NOCTURNAL HEMOGLOBINURIA; SCHOOL CHILD; THROMBOSIS;

ADOLESCENT; ANEMIA, APLASTIC; CHILD; FEMALE; HEMOGLOBINURIA, PAROXYSMAL; HUMANS; IMMUNOSUPPRESSIVE AGENTS; MALE; RETROSPECTIVE STUDIES; SEX FACTORS; SURVIVAL RATE; THROMBOSIS; TREATMENT OUTCOME;

EID: 51349161060     PISSN: 00195456     EISSN: None     Source Type: Journal    
DOI: 10.1007/s12098-008-0111-9     Document Type: Article

References (23)

1. R.L. Paquette R. Yoshimura C. Veiseh L. Kunkel J. Gajewski P.J. Rosen 1997 Clinical characteristics predict response to antithymocyte globulin in paroxysmal nocturnal hemoglobinuria Br J Haematol 96 92 97
2. G. Socié J.Y. Mary A.D. Gramont B. Rio M. Leporrier C. Rose 1996 Paroxysmal nocturnal haemoglobinuria: long-term follow-up and prognostic factors Lancet 348 573 577
3. M.M.V. Heuvel-Eibrink R.G.M. Bredius M.L. Winkel R. Tamminga J. Kraker A.Y.N. Schouten-van Meeteren 2005 Childhood paroxysmal nocturnal haemoglobinuria (PNH), a report of 11 cases in the Netherlands Br J Haematol 128 571 577
4. C. Hall S.J. Richards P. Hillmen 2002 The glycosyl-phosphatidylinositol anchor and paroxysmal nocturnal haemoglobinuria/ aplasia model Acta Haematologica 108 219 230
5. D.R. Miller R.L. Baehner L.K. Diamond 1967 Paroxysmal nocturnal hemoglobinuria in childhood and adolescence. Clinical and erythrocyte metabolic studies in two cases Pediatrics 39 675 688
6. M. Kletzel W.C. Arnold D.H. Berry 1987 Paroxysmal nocturnal hemoglobinuria presenting as recurrent hemolytic uremic syndrome Clin Pediatr 26 319 320
7. R.E. Ware S.E. Hall W.F. Rosse 1991 Paroxysmal nocturnal hemoglobinuria with onset in childhood and adolescence N Engl J Med 325 991 996
8. H.A. Wyatt A.P. Mowat M. Layton 1995 Paroxysmal nocturnal haemoglobinuria and Budd-Chiari syndrome Arch Dis Child 72 241 242
9. M.L. Graham W.F. Rosse E.C. Halperin C.R. Miller R.E. Ware 1996 Resolution of Budd-Chiari syndrome following bone marrow transplantation for paroxysmal nocturnal haemoglobinuria Br J Haematol 92 707 710
10. M. Endo P.G. Beatty T.M. Vreeke C.T. Wittwer S.P. Singh C.J. Parker 1996 Syngeneic bone marrow transplantation without conditioning in a patient with paroxysmal nocturnal hemoglobinuria: in vivo evidence that the mutant stem cells have a survival advantage Blood 88 742 750
11. H.C. Lin R.L. Chen P.J. Wang 1996 Paroxysmal nocturnal hemoglobinuria presenting as moyamoya syndrome Brain Develop 18 157 159
12. C. Flotho B. Strahm U. Kontny U. Duffner A.M. Peters W. Dupuis C.M. Niemeyer 2002 Stem cell transplantation for paroxysmal nocturnal haemoglobinuria in childhood Br J Haematol 118 124 127
13. S. Rizk I.Y. Ibrahim I.M. Mansour D. Kandil 2002 Screening for paroxysmal nocturnal hemoglobinuria (PNH) clone in Egyptian children with aplastic anemia J Trop Pediatr 48 132 137
14. L. Wainwright R.A. Brodsky L.K. Erasmus S. Poyiadjis G. Naidu D. MacKinnon 2003 Paroxysmal nocturnal hemoglobinuria arising from Fanconi anemia J Pediatr Hematol Oncol 25 167 168
15. V. Gupta V. Tilak S.V. Ramakrishna B.D. Bhatia 2006 Paroxysmal nocturnal hemoglobinuria in childhood: An uncommon presentation Indian J Med Sci 60 64 67
16. P.R. Koduri S. Gowrishankar 1992 Paroxysmal nocturnal haemoglobinuria in Indias Acta Haematol 88 126 128
17. N. Verma G. Garewal S. Verma H. Vohra 2000 Flowcytometric detection of PNH defect in Indian patients with aplastic anemia and myelodysplastic syndromes Am J Hematol 65 264 265
18. J. Nishimura R.E. Ware A. Burnette A.L. Pendleton K. Kitano T. Hirota 2002 The hematopoietic defect in PNH is not due to defective stroma, but is due to defective progenitor cells Blood Cells Mol Dis 29 159 167
19. N.S. Young J.P. Maciejewski E. Sloand G. Chen W. Zeng A. Risitano 2002 The relationship of aplastic anemia and PNH Int J Hematol 76 Suppl.2 168 172
20. H. Wang T. Chuhjo S. Yasue M. Omine S. Nakao 2002 Clinical significance of a minor population of paroxysmal nocturnal hemoglobinuria-type cells in bone marrow failure syndrome Blood 100 3897 3902
21. M. Kruatrachue P. Wasi S. Na-Nakorn 1978 Paroxysmal nocturnal haemoglobinuria in Thailand with special reference to as association with aplastic anaemia Br J Haematol 39 267 276
22. C. Hall S. Richards P. Hillmen 2003 Primary prophylaxis with warfarin prevents thrombosis in paroxysmal nocturnal hemoglobinuria (PNH) Blood 102 3587 3591
23. R.K. Marwaha D. Bansal A. Trehan N. Varma 2004 Androgens in childhood acquired aplastic anemia in Chandigarh, India Tropical Doctor 34 149 152