Medical Management and Dialysis Therapy for the Infant With an Inborn Error of Metabolism

Seminars in Nephrology

Volumn 28, Issue 5, 2008, Pages 477-480

  Picca, Stefano ^a   Bartuli, Andrea ^a   Dionisi Vici, Carlo ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

continuous arteriovenous hemodialysis; continuous venovenous hemodialysis; hemodialysis; Hyperammonemia; organic acidurias; urea cycle defects

Indexed keywords

AMMONIA; ARGININE; BENZOIC ACID; BIOTIN; CARBAMYLGLUTAMATE; CARNITINE; CYANOCOBALAMIN; FRUCTOSE 1,6 BISPHOSPHATE; GLUCOSE; GLUTAMIC ACID DERIVATIVE; HYDROXOCOBALAMIN; INSULIN; THIAMINE; UNCLASSIFIED DRUG;

ACIDURIA; ADD ON THERAPY; AMMONIA BLOOD LEVEL; ARTICLE; CALORIC INTAKE; CHILD CARE; CLINICAL DECISION MAKING; CONTINUOUS HEMODIAFILTRATION; CONTINUOUS HEMODIALYSIS; CONTINUOUS INFUSION; CONTINUOUS RENAL REPLACEMENT THERAPY; EARLY INTERVENTION; HUMAN; HYPERAMMONEMIA; INBORN ERROR OF METABOLISM; LOADING DRUG DOSE; NEWBORN INTENSIVE CARE; PATHOPHYSIOLOGY; PEDIATRICIAN; PERITONEAL DIALYSIS; PRIORITY JOURNAL; RENAL REPLACEMENT THERAPY; TREATMENT WITHDRAWAL; UREA CYCLE; VITAMIN SUPPLEMENTATION;

HUMANS; INFANT, NEWBORN; KIDNEY FAILURE, ACUTE; METABOLISM, INBORN ERRORS; RENAL DIALYSIS; TREATMENT OUTCOME;

EID: 51249104673     PISSN: 02709295     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.semnephrol.2008.05.007     Document Type: Article

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